Lipase 4
Lipase 5
Maintenance of
mitochondrial
morphology
protein 1
Mitochondrial
distribution
and morphology
protein 12
Mitochondrial
distribution
and morphology
protein 10
Mitochondrial
distribution
and morphology
protein 34
Mitochondrial
distribution
and morphology
protein 35
Glycerol-3-
phosphate
dehydrogenase
GPD2
Glycerol-3-
phosphate O-
acyltransferase
2
Glycerol-3-
phosphate O-
acyltransferase
1
Acyl- CoA:lyso-
phospholipid
acyltransferase
Probable
1-acyl-sn-
glycerol-3-
phosphate
acyltransferase
Lysophosphatidic
acid:oleoyl-CoA
acyltransferase
1
Phosphatidate
cytidylyltransferase,
mitochondrial
Phosphatidylglycerophosphatase
GEP4,
mitochondrial
CDP-
diacylglycerol-
-glycerol-3-
phosphate 3-
phosphatidyltransferase
Cardiolipin
synthase
(CMP-forming)
Cardiolipin-
specific
deacylase 1,
mitochondrial
Lysophosphatidylcholine
acyltransferase
Dihydroxyacetone
phosphate
NADH
H+
Glycerol
3-phosphate
NAD
CoA
CoA
Cytidine
triphosphate
H+
PPi
H2O
Pi
Glycerol
3-phosphate
H+
Cytidine
monophosphate
Cytidine
monophosphate
H+
H2O
1,2-Diacyl-
sn-glycerol
3-phosphate
1,2-Diacyl-
sn-glycerol
3-phosphate
1,2-Diacyl-
sn-glycerol
3-phosphate
Long-chain
fatty acyl-CoA
1-Acyl-sn-
glycerol
3-phosphate
Long-chain
fatty acyl-CoA
a CDP-
diacylglycerol
an L-1-
phosphatidylglycerol-
phosphate
an L-1-
phosphatidyl-
glycerol
a CDP-
diacylglycerol
a Cardiolipin
1-
Monolysocardiolipin
Fatty Acid
Phosphatidylcholine
a Cardiolipin
LysoPC
Protein UPS1,
mitochondrial
Endoplasmic Reticulum
Membrane
Mitochondria
Cytoplasm
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