Glutamate dehydrogenase 1, mitochondrial
Probable inactive 1-aminocyclopropane-1-carboxylate synthase-like protein 2
Aspartate aminotransferase, mitochondrial
L-Aspartic acid + Oxoglutaric acid ↔ L-Glutamic acid + Oxalacetic acid
L-Arginine + Water → Ornithine + Urea
2 Adenosine triphosphate + Ammonia + Carbon dioxide + Water → 2 Adenosine diphosphate + Carbamoyl phosphate + Phosphoric acid
Carbamoyl phosphate + Ornithine → Citrulline + Phosphate
L-Glutamic acid + NAD + Water → Ammonia + NADH + Oxoglutaric acid
L-Glutamine + Water → Ammonia + L-Glutamic acid
Adenosine triphosphate + Citrulline + L-Aspartic acid → Adenosine monophosphate + Argininosuccinic acid + Pyrophosphate
2 Argininosuccinic acid → Fumaric acid + L-Arginine
Ornithine (→), Citrulline (←) Transport: Mus musculus, Cell, Cytoplasm to Mus musculus, Cell, Mitochondrial Matrix
L-Glutamine (→) Transport: Mus musculus, Extracellular Space to Mus musculus, Cell, Cytoplasm
L-Alanine (→) Transport: Mus musculus, Extracellular Space to Mus musculus, Cell, Cytoplasm
Ornithine carbamoyltransferase, mitochondrial
Glutaminase kidney isoform, mitochondrial
L-Aspartic acid (→), L-Glutamic acid (←) Transport: Mus musculus, Cell, Mitochondrial Matrix to Mus musculus, Cell, Mitochondrial Intermembrane Space
L-Alanine + Oxoglutaric acid ↔ L-Glutamic acid + Pyruvic acid