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Carnitine O-
palmitoyltransferase
2,
mitochondrial
Enoyl-CoA
hydratase,
mitochondrial
Trifunctional
enzyme subunit
alpha,
mitochondrial
Trifunctional
enzyme subunit
beta,
mitochondrial
3-ketoacyl-CoA
thiolase,
mitochondrial
Carnitine O-
palmitoyltransferase
1, liver
isoform
Long-chain-
fatty-acid--
CoA ligase 1
Enoyl-CoA
hydratase,
mitochondrial
Trifunctional
enzyme subunit
alpha,
mitochondrial
Trifunctional
enzyme subunit
beta,
mitochondrial
3-ketoacyl-CoA
thiolase,
mitochondrial
Trifunctional
enzyme subunit
alpha,
mitochondrial
Trifunctional
enzyme subunit
beta,
mitochondrial
3-ketoacyl-CoA
thiolase,
mitochondrial
Enoyl-CoA
hydratase,
mitochondrial
Trifunctional
enzyme subunit
alpha,
mitochondrial
Trifunctional
enzyme subunit
beta,
mitochondrial
3-ketoacyl-CoA
thiolase,
mitochondrial
Enoyl-CoA
hydratase,
mitochondrial
Trifunctional
enzyme subunit
alpha,
mitochondrial
Trifunctional
enzyme subunit
beta,
mitochondrial
3-ketoacyl-CoA
thiolase,
mitochondrial
Long-chain
specific
acyl-CoA
dehydrogenase,
mitochondrial
Medium-chain
specific
acyl-CoA
dehydrogenase,
mitochondrial
Short/branched
chain specific
acyl-CoA
dehydrogenase,
mitochondrial
Short-chain
specific
acyl-CoA
dehydrogenase,
mitochondrial
Enoyl-CoA
hydratase,
mitochondrial
Trifunctional
enzyme subunit
alpha,
mitochondrial
Trifunctional
enzyme subunit
beta,
mitochondrial
3-ketoacyl-CoA
thiolase,
mitochondrial
Long-chain
specific
acyl-CoA
dehydrogenase,
mitochondrial
Medium-chain
specific
acyl-CoA
dehydrogenase,
mitochondrial
Short/branched
chain specific
acyl-CoA
dehydrogenase,
mitochondrial
Enoyl-CoA
hydratase,
mitochondrial
Acetyl-CoA
acetyltransferase,
mitochondrial
Glutaryl-CoA
dehydrogenase,
mitochondrial
Trifunctional
enzyme subunit
alpha,
mitochondrial
Trifunctional
enzyme subunit
beta,
mitochondrial
Very
long-chain
specific
acyl-CoA
dehydrogenase,
mitochondrial
Long-chain
specific
acyl-CoA
dehydrogenase,
mitochondrial
Medium-chain
specific
acyl-CoA
dehydrogenase,
mitochondrial
Long-chain
specific
acyl-CoA
dehydrogenase,
mitochondrial
Medium-chain
specific
acyl-CoA
dehydrogenase,
mitochondrial
Long-chain
specific
acyl-CoA
dehydrogenase,
mitochondrial
Medium-chain
specific
acyl-CoA
dehydrogenase,
mitochondrial
Enoyl-CoA
hydratase,
mitochondrial
Long-chain
specific
acyl-CoA
dehydrogenase,
mitochondrial
Medium-chain
specific
acyl-CoA
dehydrogenase,
mitochondrial
Long-chain
specific
acyl-CoA
dehydrogenase,
mitochondrial
Medium-chain
specific
acyl-CoA
dehydrogenase,
mitochondrial
Palmitic acid
L-Palmitoylcarnitine
L-Palmitoylcarnitine
Palmityl-CoA
L-Carnitine
CoA
(S)-3-Hydroxyhexadecanoyl-CoA
(2E)-Hexadecenoyl-CoA
H
2
O
NAD
3-Oxohexadecanoyl-CoA
NADH
H
+
Tetradecanoyl-CoA
Acetyl-CoA
CoA
Palmityl-CoA
L-Carnitine
CoA
ATP
CoA
AMP
PP
i
(S)-3-Hydroxytetradecanoyl-CoA
(2E)-Tetradecenoyl-CoA
H
2
O
NAD
3-Oxotetradecanoyl-CoA
NADH
H
+
Lauroyl-CoA
Acetyl-CoA
CoA
(S)-3-Hydroxydodecanoyl-CoA
NAD
3-Oxododecanoyl-CoA
NADH
H
+
Decanoyl-CoA
Acetyl-CoA
CoA
(S)-Hydroxydecanoyl-CoA
(2E)-Decenoyl-CoA
H
2
O
NAD
3-Oxodecanoyl-CoA
H
+
NADH
Octanoyl-CoA
Acetyl-CoA
CoA
(S)-Hydroxyoctanoyl-CoA
(2E)-Octenoyl-CoA
H
2
O
NAD
3-Oxooctanoyl-CoA
H
+
NADH
Acetyl-CoA
Hexanoyl-CoA
CoA
trans-2-Hexenoyl-CoA
(S)-Hydroxyhexanoyl-CoA
H
2
O
NAD
3-Oxohexanoyl-CoA
NADH
H
+
Acetyl-CoA
Butyryl-CoA
CoA
Crotonoyl-CoA
3-Hydroxybutyryl-CoA
H
2
O
Acetyl-CoA
Acetoacetyl-CoA
CoA
Glutaryl-CoA
CO
2
NAD
NADH
H
+
(2E)-Tetradecenoyl-CoA
H
2
O
Magnesium
FAD
FAD
FAD
FAD
FAD
FAD
FAD
FAD
FAD
FAD
FAD
FAD
FAD
FAD
FAD
FAD
FAD
FAD
FAD
electron-
transfer
flavoprotein
Reduced
electron-
transfer
flavoprotein
electron-
transfer
flavoprotein
Reduced
electron-
transfer
flavoprotein
electron-
transfer
flavoprotein
Reduced
electron-
transfer
flavoprotein
electron-
transfer
flavoprotein
Reduced
electron-
transfer
flavoprotein
electron-
transfer
flavoprotein
Reduced
electron-
transfer
flavoprotein
electron-
transfer
flavoprotein
Reduced
electron-
transfer
flavoprotein
Fatty Acid
Elongation in
Mitochondria
Glycerolipid
Metabolism
Phospholipid
Biosynthesis
Mitochondrial Matrix
Inner Mitochondria Membrane
Mitochondrial Intermembrane
Space
Outer Mitochondria Membrane
Intracellular Space
Extracellular Space
Mitochondria
CPT2
ECHS1
HADHA
HADHB
ACAA2
CPT1A
ACSL1
ECHS1
HADHA
HADHB
ACAA2
HADHA
HADHB
ACAA2
ECHS1
HADHA
HADHB
ACAA2
ECHS1
HADHA
HADHB
ACAA2
ACADL
ACADM
ACADSB
ACADS
ECHS1
HADHA
HADHB
ACAA2
ACADL
ACADM
ACADSB
ECHS1
ACAT1
GCDH
HADHA
HADHB
ACADVL
ACADL
ACADM
ACADL
ACADM
ACADL
ACADM
ECHS1
ACADL
ACADM
ACADL
ACADM
Palmitic acid
L-
Palmitoylcarnitine
L-
Palmitoylcarnitine
Palmityl-CoA
L-Carnitine
Coenzyme A
(S)-3-
Hydroxyhexadecanoyl-
CoA
(2E)-
Hexadecenoyl-
CoA
Water
NAD
3-
Oxohexadecanoyl-
CoA
NADH
Hydrogen Ion
Tetradecanoyl-
CoA
Acetyl-CoA
Coenzyme A
Palmityl-CoA
L-Carnitine
Coenzyme A
Adenosine
triphosphate
Coenzyme A
Adenosine
monophosphate
Pyrophosphate
(S)-3-
Hydroxytetradecanoyl-
CoA
(2E)-
Tetradecenoyl-
CoA
Water
NAD
3-
Oxotetradecanoyl-
CoA
NADH
Hydrogen Ion
Lauroyl-CoA
Acetyl-CoA
Coenzyme A
(S)-3-
Hydroxydodecanoyl-
CoA
NAD
3-
Oxododecanoyl-
CoA
NADH
Hydrogen Ion
Decanoyl-CoA
Acetyl-CoA
Coenzyme A
(S)-
Hydroxydecanoyl-
CoA
(2E)-
Decenoyl-CoA
Water
NAD
3-
Oxodecanoyl-
CoA
Hydrogen Ion
NADH
Octanoyl-CoA
Acetyl-CoA
Coenzyme A
(S)-
Hydroxyoctanoyl-
CoA
(2E)-
Octenoyl-CoA
Water
NAD
3-
Oxooctanoyl-
CoA
Hydrogen Ion
NADH
Acetyl-CoA
Hexanoyl-CoA
Coenzyme A
trans-2-
Hexenoyl-CoA
(S)-
Hydroxyhexanoyl-
CoA
Water
NAD
3-
Oxohexanoyl-
CoA
NADH
Hydrogen Ion
Acetyl-CoA
Butyryl-CoA
Coenzyme A
Crotonoyl-CoA
3-
Hydroxybutyryl-
CoA
Water
Acetyl-CoA
Acetoacetyl-CoA
Coenzyme A
Glutaryl-CoA
Carbon dioxide
NAD
NADH
Hydrogen Ion
(2E)-
Tetradecenoyl-
CoA
Water
electron-
transfer
flavoprotein
Reduced
electron-
transfer
flavoprotein
electron-
transfer
flavoprotein
Reduced
electron-
transfer
flavoprotein
electron-
transfer
flavoprotein
Reduced
electron-
transfer
flavoprotein
electron-
transfer
flavoprotein
Reduced
electron-
transfer
flavoprotein
electron-
transfer
flavoprotein
Reduced
electron-
transfer
flavoprotein
electron-
transfer
flavoprotein
Reduced
electron-
transfer
flavoprotein
Fatty Acid
Elongation in
Mitochondria
Glycerolipid
Metabolism
Phospholipid
Biosynthesis