Acylcarnitine (2R,3S)-3-Hydroxy-2-methylbutanoylcarnitine
Mitochondrial carnitine/acylcarnitine carrier protein
Malonyl-CoA → Acetyl-CoA + Carbon dioxide
(2R,3S)-3-Hydroxy-2-methylbutanoylcarnitine (→) Transport: Homo sapiens, Cell, Mitochondrial Intermembrane Space to Homo sapiens, Liver, Mitochondrial Matrix
(2R,3S)-3-hydroxy-2-methylbutanoic acid (→) Transport: Homo sapiens, Extracellular Space to Homo sapiens, Cell
Malonyl-CoA inhibits Carnitine O-palmitoyltransferase 1
Acetyl-CoA + L-Carnitine ↔ Coenzyme A + L-Acetylcarnitine
Carnitine O-palmitoyltransferase 1, liver isoform
Carnitine O-palmitoyltransferase 2, mitochondrial
Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids
L-Carnitine (→) Transport: Homo sapiens, Extracellular Space to Homo sapiens, Cytosol
Malonyl-CoA decarboxylase, mitochondrial
Long-chain fatty acid transport protein 1
(2R,3S)-3-Hydroxy-2-methylbutanoylcarnitine + Coenzyme A → (2R,3S)-3-Hydroxy-2-methylbutanoyl-CoA + L-Carnitine
(2R,3S)-3-Hydroxy-2-methylbutanoyl-CoA + L-Carnitine ↔ (2R,3S)-3-Hydroxy-2-methylbutanoylcarnitine + Coenzyme A
(2R,3S)-3-hydroxy-2-methylbutanoic acid + Adenosine triphosphate + Coenzyme A → (2R,3S)-3-Hydroxy-2-methylbutanoyl-CoA + Adenosine monophosphate + Pyrophosphate