(2S)-2-amino-4-{[(1R)-1-[(carboxymethyl)carbamoyl]-2-[(hydroxymethyl)sulfanyl]ethyl]carbamoyl}butanoic acid (→) Transport: Homo sapiens, Extracellular Space to Homo sapiens, Cell
(2S)-2-amino-4-{[(1R)-1-[(carboxymethyl)carbamoyl]-2-[(hydroxymethyl)sulfanyl]ethyl]carbamoyl}butanoylcarnitine (→) Transport: Homo sapiens, Cell, Mitochondrial Intermembrane Space to Homo sapiens, Liver, Mitochondrial Matrix
Mitochondrial carnitine/acylcarnitine carrier protein
Malonyl-CoA → Acetyl-CoA + Carbon dioxide
Acylcarnitine (2S)-2-amino-4-{[(1R)-1-[(carboxymethyl)carbamoyl]-2-[(hydroxymethyl)sulfanyl]ethyl]carbamoyl}butanoylcarnitine
Malonyl-CoA inhibits Carnitine O-palmitoyltransferase 1
Acetyl-CoA + L-Carnitine ↔ Coenzyme A + L-Acetylcarnitine
(2S)-2-amino-4-{[(1R)-1-[(carboxymethyl)carbamoyl]-2-[(hydroxymethyl)sulfanyl]ethyl]carbamoyl}butanoic acid
Carnitine O-palmitoyltransferase 1, liver isoform
Carnitine O-palmitoyltransferase 2, mitochondrial
Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids
L-Carnitine (→) Transport: Homo sapiens, Extracellular Space to Homo sapiens, Cytosol
Malonyl-CoA decarboxylase, mitochondrial
Long-chain fatty acid transport protein 1
(2S)-2-amino-4-{[(1R)-1-[(carboxymethyl)carbamoyl]-2-[(hydroxymethyl)sulfanyl]ethyl]carbamoyl}butanoyl-CoA + L-Carnitine ↔ (2S)-2-amino-4-{[(1R)-1-[(carboxymethyl)carbamoyl]-2-[(hydroxymethyl)sulfanyl]ethyl]carbamoyl}butanoylcarnitine + Coenzyme A
(2S)-2-amino-4-{[(1R)-1-[(carboxymethyl)carbamoyl]-2-[(hydroxymethyl)sulfanyl]ethyl]carbamoyl}butanoic acid + Adenosine triphosphate + Coenzyme A → (2S)-2-amino-4-{[(1R)-1-[(carboxymethyl)carbamoyl]-2-[(hydroxymethyl)sulfanyl]ethyl]carbamoyl}butanoyl-CoA + Adenosine monophosphate + Pyrophosphate
(2S)-2-amino-4-{[(1R)-1-[(carboxymethyl)carbamoyl]-2-[(hydroxymethyl)sulfanyl]ethyl]carbamoyl}butanoylcarnitine + Coenzyme A → (2S)-2-amino-4-{[(1R)-1-[(carboxymethyl)carbamoyl]-2-[(hydroxymethyl)sulfanyl]ethyl]carbamoyl}butanoyl-CoA + L-Carnitine