(2S,3R)-3-hydroxy-2-methylpentanedioyl-CoA + L-Carnitine ↔ (2S,3R)-3-hydroxy-2-methylpentanedioylcarnitine + Coenzyme A
(2S,3R)-3-hydroxy-2-methylpentanedioic acid + Adenosine triphosphate + Coenzyme A → (2S,3R)-3-hydroxy-2-methylpentanedioyl-CoA + Adenosine monophosphate + Pyrophosphate
(2S,3R)-3-hydroxy-2-methylpentanedioylcarnitine + Coenzyme A → (2S,3R)-3-hydroxy-2-methylpentanedioyl-CoA + L-Carnitine
Mitochondrial carnitine/acylcarnitine carrier protein
Malonyl-CoA → Acetyl-CoA + Carbon dioxide
Malonyl-CoA inhibits Carnitine O-palmitoyltransferase 1
Acetyl-CoA + L-Carnitine ↔ Coenzyme A + L-Acetylcarnitine
Carnitine O-palmitoyltransferase 1, liver isoform
Carnitine O-palmitoyltransferase 2, mitochondrial
Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids
(2S,3R)-3-hydroxy-2-methylpentanedioic acid
L-Carnitine (→) Transport: Homo sapiens, Extracellular Space to Homo sapiens, Cytosol
Malonyl-CoA decarboxylase, mitochondrial
Acylcarnitine (2S,3R)-3-hydroxy-2-methylpentanedioylcarnitine
Long-chain fatty acid transport protein 1
(2S,3R)-3-hydroxy-2-methylpentanedioylcarnitine (→) Transport: Homo sapiens, Cell, Mitochondrial Intermembrane Space to Homo sapiens, Liver, Mitochondrial Matrix
(2S,3R)-3-hydroxy-2-methylpentanedioic acid (→) Transport: Homo sapiens, Extracellular Space to Homo sapiens, Cell