Trifunctional enzyme subunit alpha, mitochondrial
Trifunctional enzyme subunit beta, mitochondrial
Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial
Medium-chain specific acyl-CoA dehydrogenase, mitochondrial
Short-chain specific acyl-CoA dehydrogenase, mitochondrial
Acetyl-CoA acetyltransferase, mitochondrial
Lauroyl-CoA + electron-transfer flavoprotein → (2E)-Tetradecenoyl-CoA + Reduced electron-transfer flavoprotein
3-Hydroxydodecanoyl-CoA → (2E)-Tetradecenoyl-CoA + Water
Carnitine O-palmitoyltransferase 1, liver isoform
Carnitine O-palmitoyltransferase 2, mitochondrial
Long-chain specific acyl-CoA dehydrogenase, mitochondrial
Glutaryl-CoA dehydrogenase, mitochondrial
3-Hydroxydodecanoyl-CoA + NAD ↔ 3-oxododecanoyl-CoA + Hydrogen Ion + NADH
Acetyl-CoA + Decanoyl-CoA → 3-oxododecanoyl-CoA + Coenzyme A
3-Hydroxydecanoyl-CoA + NAD ↔ 3-oxodecanoyl-CoA + Hydrogen Ion + NADH
3-Hydroxydecanoyl-CoA ↔ (2E)-Decenoyl-CoA + Water
Acetyl-CoA + Octanoyl-CoA ↔ 3-oxodecanoyl-CoA + Coenzyme A
3-hydroxyoctanoyl-CoA + NAD ↔ 3-oxooctanoyl-CoA + Hydrogen Ion + NADH
3-hydroxyoctanoyl-CoA ↔ (2E)-Octenoyl-CoA + Water
Acetyl-CoA + Hexanoyl-CoA ↔ 3-oxooctanoyl-CoA + Coenzyme A
3-Hydroxyhexadecanoyl-CoA ↔ (2E)-Hexadecenoyl-CoA + Water
Acetyl-CoA + Tetradecanoyl-CoA ↔ 3-oxohexadecanoyl-CoA + Coenzyme A
3-Hydroxyhexadecanoyl-CoA + NAD ↔ 3-oxohexadecanoyl-CoA + Hydrogen Ion + NADH
3-Hydroxytetradecanoyl-CoA ↔ (2E)-Tetradecenoyl-CoA + Water
Very long-chain specific acyl-CoA dehydrogenase, mitochondrial
Acetyl-CoA + Lauroyl-CoA → 3-oxotetradecanoyl-CoA + Coenzyme A
3-Hydroxytetradecanoyl-CoA + NAD ↔ 3-oxotetradecanoyl-CoA + Hydrogen Ion + NADH
Glutaryl-CoA → Carbon dioxide + Crotonoyl-CoA
Octanoyl-CoA + electron-transfer flavoprotein → (2E)-Octenoyl-CoA + Reduced electron-transfer flavoprotein
Hexanoyl-CoA + electron-transfer flavoprotein → (2E)-Hexenoyl-CoA + Reduced electron-transfer flavoprotein
Decanoyl-CoA + electron-transfer flavoprotein → (2E)-Decenoyl-CoA + Reduced electron-transfer flavoprotein
Palmitoyl-CoA + electron-transfer flavoprotein → (2E)-Hexadecenoyl-CoA + Reduced electron-transfer flavoprotein
Tetradecanoyl-CoA + electron-transfer flavoprotein → (2E)-Tetradecenoyl-CoA + Reduced electron-transfer flavoprotein
Adenosine triphosphate + Coenzyme A + Palmitic acid → Adenosine monophosphate + Palmitoyl-CoA + Pyrophosphate
L-Carnitine + Palmitoyl-CoA ↔ Coenzyme A + L-Palmitoylcarnitine
3-Hydroxybutyryl-CoA + NAD ↔ Acetoacetyl-CoA + Hydrogen Ion + NADH
3-Hydroxyhexanoyl-CoA ↔ (2E)-Hexenoyl-CoA + Water
Acetyl-CoA + Butyryl-CoA → 3-oxohexanoyl-CoA + Coenzyme A
3-Hydroxyhexanoyl-CoA + NAD ↔ 3-oxohexanoyl-CoA + Hydrogen Ion + NADH
L-Palmitoylcarnitine (→) Transport: Homo sapiens, Cell, Cytoplasm to Homo sapiens, Cell, Mitochondrial Matrix
Butyryl-CoA + electron-transfer flavoprotein ↔ Crotonoyl-CoA + Reduced electron-transfer flavoprotein
3-Hydroxybutyryl-CoA ↔ Crotonoyl-CoA + Water
2 Acetyl-CoA ↔ Acetoacetyl-CoA + Coenzyme A
Medium Chain Acyl-CoA Dehydrogenase Deficiency (MCAD)