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Peroxisomal membrane protein PEX13 Peroxisomal biogenesis factor 14 Peroxisomal membrane protein PEX13 Peroxisomal biogenesis factor 14 Peroxisomal membrane protein PEX13 Peroxisomal biogenesis factor 14 Peroxisomal membrane protein PEX13 Peroxisomal biogenesis factor 14 ATP binding cassette subfamily D member 1 ATP binding cassette subfamily D member 1 Mitochondrial basic amino acids transporter Mitochondrial basic amino acids transporter Mitochondrial basic amino acids transporter Long-chain- fatty-acid-- CoA ligase ACSBG1 Aldehyde dehydrogenase, mitochondrial Acetolactate synthase-like protein Phytanoyl-CoA dioxygenase, peroxisomal Peroxisomal carnitine O- octanoyltransferase Peroxisomal carnitine O- octanoyltransferase Long-chain- fatty-acid-- CoA ligase ACSBG1 Peroxisomal carnitine O- octanoyltransferase Peroxisomal carnitine O- octanoyltransferase Carnitine O- palmitoyltransferase 2, mitochondrial Pristanoyl-CoA Propionyl-CoA Acetyl-CoA 4,8-Dimethylnonanoyl-CoA 4,8-Dimethylnonanoyl-CoA Acetyl-CoA Pristanoyl-CoA Propionylcarnitine Propionylcarnitine L- Acetylcarnitine L- Acetylcarnitine 4,8 Dimethylnonanoyl carnitine 4,8 Dimethylnonanoyl carnitine Phytanoyl-CoA Phytanoyl-CoA Propionylcarnitine L- Acetylcarnitine 4,8 Dimethylnonanoyl carnitine ATP Pristanic acid CoA ADP PPi Pristanal CoA 2-Hydroxyphytanoyl-CoA Formyl-CoA Oxoglutaric acid O2 Succinic acid CO2 L-Carnitine CoA L-Carnitine CoA CoA Phytanic acid ATP CoA ADP PPi Propionyl-CoA L-Carnitine CoA Acetyl-CoA CoA L-Carnitine CoA Magnesium Magnesium Thiamine pyrophosphate Iron Ascorbic acid Magnesium Beta Oxidation Beta Oxidation Beta Oxidation Beta Oxidation Peroxisome Mitochondria Mitochondrial Inner Membrane Mitochondrial Outer Membrane Intracellular Space Extracellular Space
Peroxisome Mitochondria PEX13 PEX14 PEX13 PEX14 PEX13 PEX14 PEX13 PEX14 ABCD1 ABCD1 SLC25A29 SLC25A29 SLC25A29 ACSBG1 ALDH2 ILVBL PHYH CROT CROT ACSBG1 CROT CROT CPT2 Pristanoyl-CoA Propionyl-CoA Acetyl-CoA 4,8- Dimethylnonanoyl- CoA 4,8- Dimethylnonanoyl- CoA Acetyl-CoA Pristanoyl-CoA Propionylcarnitine Propionylcarnitine L- Acetylcarnitine L- Acetylcarnitine 4,8 Dimethylnonanoyl carnitine 4,8 Dimethylnonanoyl carnitine Phytanoyl-CoA Phytanoyl-CoA Propionylcarnitine L- Acetylcarnitine 4,8 Dimethylnonanoyl carnitine Adenosine triphosphate Pristanic acid Coenzyme A Adenosine diphosphate Pyrophosphate Pristanal Coenzyme A 2- Hydroxyphytanoyl- CoA Formyl-CoA Oxoglutaric acid Oxygen Succinic acid Carbon dioxide L-Carnitine Coenzyme A L-Carnitine Coenzyme A Coenzyme A Phytanic acid Adenosine triphosphate Coenzyme A Adenosine diphosphate Pyrophosphate Propionyl-CoA L-Carnitine Coenzyme A Acetyl-CoA Coenzyme A L-Carnitine Coenzyme A Beta Oxidation Beta Oxidation Beta Oxidation Beta Oxidation
PEX13 PEX14 PEX13 PEX14 PEX13 PEX14 PEX13 PEX14 ABCD1 ABCD1 SLC25A29 SLC25A29 SLC25A29 ACSBG1 ALDH2 ILVBL PHYH CROT CROT ACSBG1 CROT CROT CPT2 PrisCoA PropCoA Ac-CoA 48DmnCA 48DmnCA Ac-CoA PrisCoA Propion Propion L-Alcar L-Alcar 48DnCn 48DnCn PhytCoA PhytCoA Propion L-Alcar 48DnCn ATP Pristan CoA ADP PPi Pristal CoA 2HPCoA FormCoA AKG O2 Succini CO2 L-Carnt CoA L-Carnt CoA CoA Phytana ATP CoA ADP PPi PropCoA L-Carnt CoA Ac-CoA CoA L-Carnt CoA Mg2+ Mg2+ ThiamPP Iron VitC Mg2+ Bet Oxi Bet Oxi Bet Oxi Bet Oxi Peroxisome Mitochondria Mitochondrial Inner Membrane Mitochondrial Outer Membrane Intracellular Space Extracellular Space
Peroxisome Mitochondria PEX13 PEX14 PEX13 PEX14 PEX13 PEX14 PEX13 PEX14 ABCD1 ABCD1 SLC25A29 SLC25A29 SLC25A29 ACSBG1 ALDH2 ILVBL PHYH CROT CROT ACSBG1 CROT CROT CPT2 PrisCoA PropCoA Ac-CoA 48DmnCA 48DmnCA Ac-CoA PrisCoA Propion Propion L-Alcar L-Alcar 48DnCn 48DnCn PhytCoA PhytCoA Propion L-Alcar 48DnCn ATP Pristan CoA ADP Ppi Pristal CoA 2HPCoA FormCoA AKG O2 Succini CO2 L-Carnt CoA L-Carnt CoA CoA Phytana ATP CoA ADP Ppi PropCoA L-Carnt CoA Ac-CoA CoA L-Carnt CoA Bet Oxi Bet Oxi Bet Oxi Bet Oxi