2-amino-3-
carboxymuconate-
6-semialdehyde
decarboxylase
2-aminomuconic
semialdehyde
dehydrogenase
Unknown
Unknown
Probable
2-oxoglutarate
dehydrogenase E1
component DHKTD1,
mitochondrial
Dihydrolipoyllysine-
residue
succinyltransferase
component of
2-oxoglutarate
dehydrogenase
complex,
mitochondrial
Dihydrolipoyl
dehydrogenase,
mitochondrial
2-Amino-3-
carboxymuconic
acid semialdehyde
Glutaryl-CoA
H+
2-Aminomuconic
acid semialdehyde
CO2
H2O
NAD
2-Aminomuconic
acid
H+
NADH
H2O
(3E)-2-oxohex-
3-enedioate
Ammonium
H+
NADH
Oxoadipic acid
NAD
CoA
NAD
NADH
CO2
Thiamine
pyrophosphate
Lipoamide
FAD
L-tryptophan
degradation
Glutaryl-CoA
degradation
Mitochondria
Cytosol
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