Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial
Sodium-coupled neutral amino acid transporter 4
4-aminobutyrate aminotransferase, mitochondrial
Ureidopropionic acid + Water ↔ Ammonia + Carbon dioxide + β-Alanine
β-Alanine (→) Transport: Homo sapiens, Intestine to Homo sapiens, Liver, Hepatocyte, Mitochondrial Matrix
Dihydropyrimidine dehydrogenase [NADP(+)]
L-Aspartic acid → Carbon dioxide + β-Alanine
Oxoglutaric acid + β-Alanine → L-Glutamic acid + Malonic semialdehyde
Mitochondrial carnitine/acylcarnitine carrier protein CACL
Dihydrouracil + NADP ↔ NADPH + Uracil
Coenzyme A + Malonic semialdehyde + NAD → Acetyl-CoA + Carbon dioxide + NADH
Anserine + Water → 3-Methylhistidine + β-Alanine
Carnosine + Water → L-Histidine + β-Alanine
3-Aminopropionaldehyde + NAD + Water → Hydrogen Ion + NADH + β-Alanine
Dihydrouracil + Water ↔ Ureidopropionic acid
1,3-Diaminopropane + Oxygen + Water → 3-Aminopropionaldehyde + Ammonia + Hydrogen peroxide