Uroporphyrin I (→) Transport: Homo sapiens, Cell, Cytosol to Homo sapiens, Blood Vessel
Protoporphyrin IX (←) Transport: Homo sapiens, Cell, Mitochondrial Inner Membrane to Homo sapiens, Cell, Mitochondrial Matrix
5-aminolevulinate synthase, nonspecific, mitochondrial
Congenital Erythropoietic Porphyria (CEP) or Gunther Disease
Coproporphyrinogen III (→) Transport: Homo sapiens, Cell, Cytosol to Homo sapiens, Cell, Mitochondrion
Coproporphyrinogen-III oxidase, mitochondrial
Feline leukemia virus subgroup C receptor-related protein 2
Heme (→) Transport: Homo sapiens, Cell, Mitochondrion to Homo sapiens, Cell, Cytoplasm
Protoheme IX farnesyltransferase, mitochondrial
Farnesyl pyrophosphate + Heme → Heme O
Cytochrome c oxidase assembly protein COX15 homolog
Bilirubin diglucuronide + Water → Alcohol + Urobilinogen
Bilirubin + Uridine diphosphate glucuronic acid → Bilirubin diglucuronide + Uridine 5'-diphosphate
Biliverdin + NAD → Bilirubin + NADH
3 AH2 + Heme + 3 Oxygen → 3 A + Biliverdin + Carbon monoxide + Fe2+ + 3 Water
Hydroxymethylbilane → Uroporphyrinogen III + Water
Hydroxymethylbilane → Uroporphyrinogen I
Uroporphyrinogen III → Uroporphyrin III
4 Porphobilinogen + Water → 4 Ammonia + Hydroxymethylbilane
Glycine + Succinyl-CoA → 5-Aminolevulinic acid + Carbon dioxide
5-Aminolevulinic acid → Porphobilinogen + 2 Water
3 Oxygen + Protoporphyrinogen IX → 3 Hydrogen peroxide + Protoporphyrin IX
4 Fe2+ + 4 Hydrogen + Oxygen ← 4 Fe3+ + 2 Water
Fe2+ + Protoporphyrin IX → Heme + 2 Hydrogen
Uroporphyrinogen I → 4 Carbon dioxide + Coproporphyrinogen I
Coproporphyrinogen III + 2 Hydrogen + Oxygen → 2 Carbon dioxide + Protoporphyrinogen IX + 2 Water
Coproporphyrinogen III → Coproporphyrin III
Uroporphyrinogen I → Uroporphyrin I
Uroporphyrinogen III → 4 Carbon dioxide + Coproporphyrinogen III
Broad substrate specificity ATP-binding cassette transporter ABCG2
Coproporphyrinogen I → Coproporphyrin I