2-oxoisovalerate dehydrogenase subunit beta, mitochondrial
branched-chain alpha-keto dehydrogenase complex
3-Methyl-2-oxovaleric acid + Coenzyme A + NAD → 2-Methylbutyryl-CoA + Carbon dioxide
L-Isoleucine + Oxoglutaric acid → 3-Methyl-2-oxovaleric acid + L-Glutamic acid
Glycine + Tiglyl-CoA → Coenzyme A + Hydrogen + Tiglylglycine
2-Methylbutyryl-CoA + FAD + Hydrogen → FADH + Tiglyl-CoA
2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial
Metabolism and Physiological Effects of Tiglylglycine
Lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial
Dihydrolipoyl dehydrogenase, mitochondrial
Tiglylglycine (→) Transport: Homo sapiens, Cell, Mitochondrion to Homo sapiens, Blood Vessel
L-Isoleucine (→) Transport: Homo sapiens, Blood Vessel to Homo sapiens, Cell, Mitochondrion
L-Isoleucine (→) Transport: Homo sapiens to Homo sapiens, Intestine, Epithelial Cell, Cytosol
L-Isoleucine (→) Transport: Homo sapiens, Intestine, Epithelial Cell, Cytosol to Homo sapiens, Blood Vessel
Branched-chain-amino-acid aminotransferase, mitochondrial