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Search for 'valine AND leucine' in 'all pathways' in 'all' returned 483 results

SMP0457126 View Pathway	Metabolite Secondary Metabolites: Valine and L-Leucine Biosynthesis from Pyruvate Brachyspira pilosicoli B2904 Matched Description: The biosynthesis of Valine and L-leucine from pyruvic acid starts with pyruvic acid interacting … -oxovaleric acid can produce an L-valine by interacting with a L-glutamic acid through a Valine … Transaminase resulting in the release of a Oxoglutaric acid and a L-valine. The 3-methyl-2-oxovaleric acid … with a L-glutamic acid through a branched-chain amino-acid aminotransferase resulting in the oxoglutaric acid and L-leucine. Matched Compounds: L-Valine … L-Leucine Matched Compound Synonyms: (s)-valine … Valine … L-valine … Keto-leucine … (2s)-alpha-leucine BioPAX SVG SBGN SBML PWML All files (.zip) Metabolic
SMP0455574 View Pathway	Metabolite Secondary Metabolites: Valine and L-Leucine Biosynthesis from Pyruvate Fusobacterium periodonticum 1_1_41FAA Matched Description: The biosynthesis of Valine and L-leucine from pyruvic acid starts with pyruvic acid interacting … -oxovaleric acid can produce an L-valine by interacting with a L-glutamic acid through a Valine … Transaminase resulting in the release of a Oxoglutaric acid and a L-valine. The 3-methyl-2-oxovaleric acid … with a L-glutamic acid through a branched-chain amino-acid aminotransferase resulting in the oxoglutaric acid and L-leucine. Matched Compounds: L-Valine … L-Leucine Matched Compound Synonyms: (s)-valine … Valine … L-valine … Keto-leucine … (2s)-alpha-leucine BioPAX SVG SBGN SBML PWML All files (.zip) Metabolic
SMP0451578 View Pathway	Metabolite Secondary Metabolites: Valine and L-Leucine Biosynthesis from Pyruvate Escherichia coli (strain SE11) Matched Description: The biosynthesis of Valine and L-leucine from pyruvic acid starts with pyruvic acid interacting … -oxovaleric acid can produce an L-valine by interacting with a L-glutamic acid through a Valine … Transaminase resulting in the release of a Oxoglutaric acid and a L-valine. The 3-methyl-2-oxovaleric acid … with a L-glutamic acid through a branched-chain amino-acid aminotransferase resulting in the oxoglutaric acid and L-leucine. Matched Compounds: L-Valine … L-Leucine Matched Compound Synonyms: (s)-valine … Valine … L-valine … Keto-leucine … (2s)-alpha-leucine BioPAX SVG SBGN SBML PWML All files (.zip) Metabolic
SMP0120523 View Pathway	Metabolite Methylmalonate Semialdehyde Dehydrogenase Deficiency Mus musculus Matched Compounds: L-Valine … L-Leucine Matched Compound Synonyms: (s)-valine … Valine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine BioPAX SVG SBGN SBML PWML All files (.zip) Disease
SMP0120525 View Pathway	Metabolite Methylmalonic Aciduria Mus musculus Matched Compounds: L-Valine … L-Leucine Matched Compound Synonyms: (s)-valine … Valine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine BioPAX SVG SBGN SBML PWML All files (.zip) Disease
SMP0120736 View Pathway	Metabolite Maple Syrup Urine Disease Rattus norvegicus Matched Description: for a protein which is vital in the breakdown of amino acids, specifically the amino acids leucine … , isoleucine and valine. This disorder is characterized by a large accumulation of these amino acids Matched Compounds: L-Valine … L-Leucine Matched Compound Synonyms: (s)-valine … Valine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine BioPAX SVG SBGN SBML PWML All files (.zip) Disease
SMP0120441 View Pathway	Metabolite 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I Mus musculus Matched Description: constitute the breakdown of leucine. Mutations in the aforementioned genes leads to a reduction in the … breakdown leucine properly. Consequently, this leads to the build up of toxic byproducts which are not … processed as the breakdown of leucine is left incomplete. If these toxic byproducts manifest themselves Matched Compounds: L-Valine … L-Leucine Matched Compound Synonyms: (s)-valine … Valine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine BioPAX SVG SBGN SBML PWML All files (.zip) Disease
SMP0120588 View Pathway	Metabolite Isobutyryl-CoA Dehydrogenase Deficiency Mus musculus Matched Description: error of metabolism (IEM) of valine metabolism. It is an autosomal recessive disorder that is caused … the metabolism of branched-chain amino acids, specifically valine. This enzyme is responsible for … the third step in the breakdown of valine and converts isobutyryl-CoA into methylacrylyl-CoA. Defects … in the IBD enzyme function lead to elevated levels of valine in blood and other biofluids … energy. Treatment may include the use of L-carnitine supplements, frequent meals, and a low-valine diet. Matched Compounds: L-Valine … L-Leucine Matched Compound Synonyms: (s)-valine … Valine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine BioPAX SVG SBGN SBML PWML All files (.zip) Disease
SMP0120745 View Pathway	Metabolite Methylmalonic Aciduria Rattus norvegicus Matched Compounds: L-Valine … L-Leucine Matched Compound Synonyms: (s)-valine … Valine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine BioPAX SVG SBGN SBML PWML All files (.zip) Disease
SMP0120757 View Pathway	Metabolite Propionic Acidemia Rattus norvegicus Matched Compounds: L-Valine … L-Leucine Matched Compound Synonyms: (s)-valine … Valine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine BioPAX SVG SBGN SBML PWML All files (.zip) Disease