SMP0124169
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Acylcarnitine (2E,4E)-Tetradecadienoylcarnitine
Homo sapiens
Matched Description: first transported into the cell via the long-chain fatty acid transport protein 1 (FATP1). Once … -CoA. This reaction is facilitated by the long-chain fatty-acid CoA ligase 1 protein, which adds a … catalyzed by acetyl-CoA carboxylase 1 to form malonyl-CoA, which inhibits the action of carnitine O … -palmitoyltransferase 1, thereby preventing (2E,4E)-tetradecadienoylcarnitine from forming and
Matched Proteins: Long-chain-fatty-acid--CoA ligase 1 … Carnitine O-palmitoyltransferase 1, liver isoform … Acetyl-CoA carboxylase 1 … Long-chain fatty acid transport protein 1
Matched Protein Synonyms: Acyl-CoA synthetase 1 … LACS 1 … Long-chain acyl-CoA synthetase 1 … Palmitoyl-CoA ligase 1
Matched Compound Synonyms: 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine
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SMP0124176
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Acylcarnitine 3-Hydroxytrtradeca-6,9-dienoylcarnitine
Homo sapiens
Matched Description: -dienoic acid is first transported into the cell via the long-chain fatty acid transport protein 1 … -hydroxytrtradeca-6,9-dienoyl-CoA. This reaction is facilitated by the long-chain fatty-acid CoA ligase 1 … circumstances. Finally, acetyl-CoA in the cytosol can be catalyzed by acetyl-CoA carboxylase 1 to form … malonyl-CoA, which inhibits the action of carnitine O-palmitoyltransferase 1, thereby preventing 3
Matched Proteins: Long-chain-fatty-acid--CoA ligase 1 … Carnitine O-palmitoyltransferase 1, liver isoform … Acetyl-CoA carboxylase 1 … Long-chain fatty acid transport protein 1
Matched Protein Synonyms: Acyl-CoA synthetase 1 … LACS 1 … Long-chain acyl-CoA synthetase 1 … Palmitoyl-CoA ligase 1
Matched Compound Synonyms: 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine
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SMP0124181
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Acylcarnitine 3-Hydroxytrtradeca-5,7-dienoylcarnitine
Homo sapiens
Matched Description: -dienoic acid is first transported into the cell via the long-chain fatty acid transport protein 1 … -hydroxytrtradeca-5,7-dienoyl-CoA. This reaction is facilitated by the long-chain fatty-acid CoA ligase 1 … circumstances. Finally, acetyl-CoA in the cytosol can be catalyzed by acetyl-CoA carboxylase 1 to form … malonyl-CoA, which inhibits the action of carnitine O-palmitoyltransferase 1, thereby preventing 3
Matched Proteins: Long-chain-fatty-acid--CoA ligase 1 … Carnitine O-palmitoyltransferase 1, liver isoform … Acetyl-CoA carboxylase 1 … Long-chain fatty acid transport protein 1
Matched Protein Synonyms: Acyl-CoA synthetase 1 … LACS 1 … Long-chain acyl-CoA synthetase 1 … Palmitoyl-CoA ligase 1
Matched Compound Synonyms: 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine
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SMP0124188
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Acylcarnitine Tetradeca-8,10,12-trienoylcarnitine
Homo sapiens
Matched Description: acid is first transported into the cell via the long-chain fatty acid transport protein 1 (FATP1). Once … -trienoyl-CoA. This reaction is facilitated by the long-chain fatty-acid CoA ligase 1 protein, which … the cytosol can be catalyzed by acetyl-CoA carboxylase 1 to form malonyl-CoA, which inhibits the … action of carnitine O-palmitoyltransferase 1, thereby preventing tetradeca-8,10,12-trienoylcarnitine
Matched Proteins: Long-chain-fatty-acid--CoA ligase 1 … Carnitine O-palmitoyltransferase 1, liver isoform … Acetyl-CoA carboxylase 1 … Long-chain fatty acid transport protein 1
Matched Protein Synonyms: Acyl-CoA synthetase 1 … LACS 1 … Long-chain acyl-CoA synthetase 1 … Palmitoyl-CoA ligase 1
Matched Compound Synonyms: 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine
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SMP0124193
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Acylcarnitine Tetradeca-5,8,11-trienoylcarnitine
Homo sapiens
Matched Description: is first transported into the cell via the long-chain fatty acid transport protein 1 (FATP1). Once … -trienoyl-CoA. This reaction is facilitated by the long-chain fatty-acid CoA ligase 1 protein, which adds a … cytosol can be catalyzed by acetyl-CoA carboxylase 1 to form malonyl-CoA, which inhibits the action of … carnitine O-palmitoyltransferase 1, thereby preventing tetradeca-5,8,11-trienoylcarnitine from forming
Matched Proteins: Long-chain-fatty-acid--CoA ligase 1 … Carnitine O-palmitoyltransferase 1, liver isoform … Acetyl-CoA carboxylase 1 … Long-chain fatty acid transport protein 1
Matched Protein Synonyms: Acyl-CoA synthetase 1 … LACS 1 … Long-chain acyl-CoA synthetase 1 … Palmitoyl-CoA ligase 1
Matched Compound Synonyms: 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine
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SMP0124195
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Acylcarnitine Tetradeca-6,8,10-trienoylcarnitine
Homo sapiens
Matched Description: is first transported into the cell via the long-chain fatty acid transport protein 1 (FATP1). Once … -trienoyl-CoA. This reaction is facilitated by the long-chain fatty-acid CoA ligase 1 protein, which adds a … cytosol can be catalyzed by acetyl-CoA carboxylase 1 to form malonyl-CoA, which inhibits the action of … carnitine O-palmitoyltransferase 1, thereby preventing tetradeca-6,8,10-trienoylcarnitine from forming
Matched Proteins: Long-chain-fatty-acid--CoA ligase 1 … Carnitine O-palmitoyltransferase 1, liver isoform … Acetyl-CoA carboxylase 1 … Long-chain fatty acid transport protein 1
Matched Protein Synonyms: Acyl-CoA synthetase 1 … LACS 1 … Long-chain acyl-CoA synthetase 1 … Palmitoyl-CoA ligase 1
Matched Compound Synonyms: 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine
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SMP0124200
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Acylcarnitine 3-Hydroxytetradeca-6,9,12-trienoylcarnitine
Homo sapiens
Matched Description: 1 (FATP1). Once inside the cell it undergoes a reaction to form an acyl-CoA derivative called 3 … ligase 1 protein, which adds a CoA moiety to appropriate acyl groups. Many acyl-CoA groups will then … by acetyl-CoA carboxylase 1 to form malonyl-CoA, which inhibits the action of carnitine O … -palmitoyltransferase 1, thereby preventing 3-hydroxytetradeca-6,9,12-trienoylcarnitine from forming and
Matched Proteins: Long-chain-fatty-acid--CoA ligase 1 … Carnitine O-palmitoyltransferase 1, liver isoform … Acetyl-CoA carboxylase 1 … Long-chain fatty acid transport protein 1
Matched Protein Synonyms: Acyl-CoA synthetase 1 … LACS 1 … Long-chain acyl-CoA synthetase 1 … Palmitoyl-CoA ligase 1
Matched Compound Synonyms: 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine
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SMP0124207
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Acylcarnitine 3-Hydroxytetradeca-4,7,10-trienoylcarnitine
Homo sapiens
Matched Description: 1 (FATP1). Once inside the cell it undergoes a reaction to form an acyl-CoA derivative called 3 … ligase 1 protein, which adds a CoA moiety to appropriate acyl groups. Many acyl-CoA groups will then … by acetyl-CoA carboxylase 1 to form malonyl-CoA, which inhibits the action of carnitine O … -palmitoyltransferase 1, thereby preventing 3-hydroxytetradeca-4,7,10-trienoylcarnitine from forming and
Matched Proteins: Long-chain-fatty-acid--CoA ligase 1 … Carnitine O-palmitoyltransferase 1, liver isoform … Acetyl-CoA carboxylase 1 … Long-chain fatty acid transport protein 1
Matched Protein Synonyms: Acyl-CoA synthetase 1 … LACS 1 … Long-chain acyl-CoA synthetase 1 … Palmitoyl-CoA ligase 1
Matched Compound Synonyms: 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine
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SMP0125588
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Sepiapterin Reductase Deficiency
Homo sapiens
Matched Compounds: 1-hydroxy-2-Oxopropyl tetrahydropterin
Matched Proteins: GTP cyclohydrolase 1 … GTP cyclohydrolase 1 feedback regulatory protein … Carbonyl reductase [NADPH] 1 … Tryptophan 5-hydroxylase 1
Matched Protein Synonyms: Aldo-keto reductase family 1 member B1 … NADPH-dependent carbonyl reductase 1 … NADPH-dependent carbonyl reductase 1 … Tryptophan 5-monooxygenase 1
Matched Compound Synonyms: (phosphate)n-1 … 2'-(dihydrogen phosphate) 5'-(trihydrogen pyrophosphate) adenosine 5'-ester with 1,4-dihydro-1-b-d-ribofuranosylnicotinamide … 2'-(dihydrogen phosphate) 5'-(trihydrogen pyrophosphate) adenosine 5'-ester with 1,4-dihydro-1-beta-delta-ribofuranosylnicotinamide … Adenosine 5'-(trihydrogen diphosphate) 2'-(dihydrogen phosphate) p'-5'-ester with 1,4-dihydro-1-beta-d-ribofuranosyl-3-pyridinecarboxamide … Adenosine 5'-(trihydrogen diphosphate) 2'-(dihydrogen phosphate) p'-5'-ester with 1,4-dihydro-1-beta-delta-ribofuranosyl-3-pyridinecarboxamide
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SMP0130741
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Stiripentol Drug Metabolism
Homo sapiens
Matched Protein Synonyms: LST-1 … Liver-specific organic anion transporter 1 … LST-1 … Liver-specific organic anion transporter 1
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