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Mitochondria
Chloroplast
Peroxisome
Branched-chain-
amino-acid
aminotransferase
1, mitochondrial
Branched-chain-
amino-acid
aminotransferase
6
Branched-chain-
amino-acid
aminotransferase
2, chloroplastic
Branched-chain-
amino-acid
aminotransferase
3, chloroplastic
Branched-chain-
amino-acid
aminotransferase
5, chloroplastic
2-oxoisovalerate
dehydrogenase
subunit alpha 2,
mitochondrial
2-oxoisovalerate
dehydrogenase
subunit beta 2,
mitochondrial
Lipoamide
acyltransferase
component of
branched-chain
alpha-keto acid
dehydrogenase
complex,
mitochondrial
Dihydrolipoyl
dehydrogenase 2,
mitochondrial
Isovaleryl-CoA
dehydrogenase,
mitochondrial
3-
hydroxyisobutyryl-
CoA hydrolase 1
Probable 3-
hydroxyisobutyrate
dehydrogenase,
mitochondrial
Methylmalonate-
semialdehyde
dehydrogenase
[acylating],
mitochondrial
α-Ketoisovaleric
acid
α-Ketoisovaleric
acid
L-Valine
Oxoglutaric acid
L-Glutamic acid
L-Valine
Oxoglutaric acid
L-Glutamic acid
L-Valine
Oxoglutaric acid
L-Glutamic acid
L-Valine
Oxoglutaric acid
L-Glutamic acid
L-Valine
Oxoglutaric acid
L-Glutamic acid
CoA
NAD
2-Methylpropanal
CO
2
NADH
FAD
H
+
FADH
2
Methacrylyl-CoA
H
2
O
(S)-3-
Hydroxyisobutyryl-
CoA
H
2
O
CoA
(S)-3-
Hydroxyisobutyric
acid
H
+
NAD
H
+
NADH
(S)-Methylmalonic
acid semialdehyde
L-Glutamic acid
Oxoglutaric acid
(S)-beta-
Aminoisobutyric
acid
H
2
O
NAD
CoA
Propionyl-CoA
NADH
H
+
HCO
3
-
Mitochondria
Chloroplast
Peroxisome
BCAT1
BCAT6
BCAT2
BCAT3
BCAT5
At5g09300
DIN4
BCE2
LPD2
IVD
CHY1
At4g20930
ALDH6B2
α-Ketoisovaleric
acid
α-Ketoisovaleric
acid
L-Valine
Oxoglutaric acid
L-Glutamic acid
L-Valine
Oxoglutaric acid
L-Glutamic acid
L-Valine
Oxoglutaric acid
L-Glutamic acid
L-Valine
Oxoglutaric acid
L-Glutamic acid
L-Valine
Oxoglutaric acid
L-Glutamic acid
Coenzyme A
NAD
2-Methylpropanal
Carbon dioxide
NADH
FAD
Hydrogen Ion
FADH
Methacrylyl-CoA
Water
(S)-3-
Hydroxyisobutyryl-
CoA
Water
Coenzyme A
(S)-3-
Hydroxyisobutyric
acid
Hydrogen Ion
NAD
Hydrogen Ion
NADH
(S)-Methylmalonic
acid semialdehyde
L-Glutamic acid
Oxoglutaric acid
(S)-beta-
Aminoisobutyric
acid
Water
NAD
Coenzyme A
Propionyl-CoA
NADH
Hydrogen Ion
Hydrogen
carbonate
Mitochondria
Chloroplast
Peroxisome
BCAT1
BCAT6
BCAT2
BCAT3
BCAT5
At5g09300
DIN4
BCE2
LPD2
IVD
CHY1
At4g20930
ALDH6B2
Ketoval
Ketoval
Val
AKG
Glu
Val
AKG
Glu
Val
AKG
Glu
Val
AKG
Glu
Val