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Serine racemase
branched-chain
alpha-keto
dehydrogenase
complex
Propionyl-CoA
carboxylase
Methylmalonyl-
CoA epimerase,
mitochondrial
Methylmalonyl-
CoA mutase,
mitochondrial
Succinyl-CoA
2-Ketobutyric
acid
L-Threonine
L-Threonine
2-Ketobutyric
acid
NH
3
Coenzyme A
NAD
Propionyl-CoA
NADH
Hydrogen
carbonate
ATP
S-Methylmalonyl-CoA
ADP
H
+
R-Methylmalonyl-CoA
Pyridoxal
5'-phosphate
Thiamine
pyrophosphate
FAD
Thiamine
pyrophosphate
Biotin
Adenosylcobalamin
Citric Acid
Cycle
Homocysteine
Degradation
Methionine
Metabolism
Extracellular space
Intracellular Space
Mitochondria
Inner mitochondrial membrane
Outer mitochondrial membrane
Mitochondria
Srr
Pdha2
Pc
Pccb
Mcee
Mut
Succinyl-CoA
2-Ketobutyric
acid
L-Threonine
L-Threonine
2-Ketobutyric
acid
Ammonia
Coenzyme A
NAD
Propionyl-CoA
NADH
Hydrogen
carbonate
Adenosine
triphosphate
S-
Methylmalonyl-
CoA
Adenosine
diphosphate
Hydrogen
R-
Methylmalonyl-
CoA
Citric Acid
Cycle
Homocysteine
Degradation
Methionine
Metabolism
Srr
Pdha2
Pc
Pccb
Mcee
Mut
Suc-CoA
2KBA
Thr
Thr
2KBA
NH
3
CoA
NAD
PropCoA
NADH
HCO3
ATP
S-MmCoA
ADP
H
+
R-MmCoA
Pyr-5'P
ThiamPP
FAD
ThiamPP
Biotin
Adnscbn
PW000005
PW000027
PW000056
Extracellular space
Intracellular Space
Mitochondria
Inner mitochondrial membrane
Outer mitochondrial membrane