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2-amino-3-
ketobutyrate
coenzyme A
ligase,
mitochondrial
Serine
palmitoyltransferase
1
3-
ketodihydrosphingosine
reductase
Sphingosine
kinase 2
Sphingosine-1-
phosphate
phosphatase 2
Phospholipid
phosphatase 2
SGPL1 protein
Sphingolipid
delta(4)-
desaturase/C4-
monooxygenase
DES2
SGPL1 protein
Sphingosine
kinase 2
Sphingosine-1-
phosphate
phosphatase 2
Phospholipid
phosphatase 2
Alkaline
ceramidase
Ceramide kinase
Phospholipid
phosphatase 2
Sphingosine-1-
phosphate
phosphatase 2
Sphingomyelin
synthase 1
Bis(5'-
adenosyl)-
triphosphatase
ENPP4
UDP-
glucuronosyltransferase
3A1
Galactosylceramidase
Glucosylceramidase
UDP-glucose
ceramide
glucosyltransferase
Unknown
Beta-1,4-
galactosyltransferase
3
Galactosylceramide
sulfotransferase
Arylsulfatase A
Alpha-N-
acetylgalactosaminidase
Galactosylceramide
sulfotransferase
Sialidase-3
ACER3 protein
L-Serine
Palmitoyl-CoA
3-
Dehydrosphinganine
Sphinganine
NADPH
NADP
ATP
ADP
Sphinganine
1-phosphate
ADP
ATP
P
i
O-
Phosphoethanolamine
Dihydroceramide
Ceramide
(d18:1/18:0)
Sphingosine
1-phosphate
Sphingosine
ATP
ADP
ADP
ATP
P
i
ATP
CerP(d18:1/12:0)
ADP
P
i
SM(d18:1/18:0)
Galactosylceramide
(d18:1/16:0)
Glucosylceramide
Lactosylceramide
(d18:1/12:0)
Phosphoadenosine
phosphosulfate
3-O-
Sulfogalactosylceramide
(d18:1/24:0)
Adenosine
3',5'-diphosphate
H
2
O
Sulfate
D-Galactose
Galabiosylceramide
(d18:1/22:0)
Phosphoadenosine
phosphosulfate
Adenosine
3',5'-diphosphate
N-
acetylneuraminyl-
Galactosylceramide
Sphinganine
Pyridoxal
5'-phosphate
Magnesium
Pyridoxal
5'-phosphate
Pyridoxal
5'-phosphate
Magnesium
Calcium
Magnesium
Magnesium
Zinc
Calcium
Galabiosylceramide-
sulfate
Glycine and
Serine
Metabolism
Intracellular space
Endoplasmic Reticulum
Golgi complex
Golgi complex
Lysosome
Lysosome
Endoplasmic Reticulum