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Malate
dehydrogenase,
mitochondrial
Unknown
Unknown
Mitochondrial
pyruvate
carrier 1
Pyruvate
dehydrogenase
complex
Citrate
synthase,
mitochondrial
Isocitrate
dehydrogenase
[NAD] subunit
alpha,
mitochondrial
Isocitrate
dehydrogenase
[NAD] subunit
gamma 1,
mitochondrial
Isocitrate
dehydrogenase
[NAD] subunit
gamma 1,
mitochondrial
Oxoglutarate
dehydrogenase
complex
Succinyl-CoA
ligase
Fumarate
hydratase,
mitochondrial
Pyruvate
carboxylase,
mitochondrial
Succinate
dehydrogenase
Aconitate
hydratase,
mitochondrial
Aconitate
hydratase,
mitochondrial
Unknown
Glutaminase
liver isoform,
mitochondrial
Isocitrate
dehydrogenase
[NADP]
cytoplasmic
Unknown
Unknown
Unknown
Cytoplasmic
aconitate
hydratase
Pyruvic acid
FADH
2
Pyruvic acid
CoA
NAD
Acetyl-CoA
CO
2
NADH
H
2
O
Oxalacetic acid
Citric acid
CoA
Isocitric acid
NAD
Oxoglutaric acid
CO
2
NADH
H
+
NAD
CoA
Succinyl-CoA
NADH
H
+
CO
2
P
i
GDP
Succinic acid
CoA
GTP
L-Malic acid
Fumaric acid
H
2
O
NAD
NADH
H
+
ATP
HCO
3
-
ADP
P
i
Q
FAD
QH
2
cis-Aconitic
acid
H
2
O
H
2
O
NADPH
Ammonium
H
+
L-Glutamic acid
H
2
O
NADP
L-Glutamine
H
2
O
NH
3
Isocitric acid
NADP
Oxoglutaric acid
NADPH
NADPH
2-Hydroxyglutarate
NADP
NADP
Oxoglutaric acid
NADPH
NADP
Oxoglutaric acid
NADPH
Citric acid
Citric acid
Thiamine
pyrophosphate
Lipoamide
FAD
Magnesium
Thiamine
pyrophosphate
Lipoamide
FAD
Biotin
Manganese
4Fe-4S
4Fe-4S
Magnesium
4Fe-4S
Glycolysis
Mitochondrial
Electron
Transport Chain
Inner mitochondrial membrane
Mitochondrial intermembrane
space
Cytosol
Mitochondrial matrix
Mitochondrion
Intracellular Space
Inner mitochondrial membrane
Outer mitochondrial membrane
Cytosol
Epigenetic Regulation
Oncogene Activation,
Tumour-suppressor
inactivation
TCA cycle
Citric acid
Isocitric acid
Oxoglutaric acid
2-Hydroxyglutarate
Cytoplasmic aconitate
hydratase
Isocitrate dehydrogenase
[NADP] cytoplasmic
mutIDH1
Methylcystosine dioxygenase
TET1
Lysine-specific demethylase
2A