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Malate dehydrogenase, mitochondrial Unknown Unknown Mitochondrial pyruvate carrier 1 Pyruvate dehydrogenase complex Citrate synthase, mitochondrial Isocitrate dehydrogenase [NAD] subunit alpha, mitochondrial Isocitrate dehydrogenase [NAD] subunit beta, mitochondrial Isocitrate dehydrogenase [NAD] subunit gamma 1, mitochondrial Oxoglutarate dehydrogenase complex Succinyl-CoA ligase Fumarate hydratase, mitochondrial Pyruvate carboxylase, mitochondrial Succinate dehydrogenase Aconitate hydratase, mitochondrial Aconitate hydratase, mitochondrial Unknown Glutaminase liver isoform, mitochondrial Isocitrate dehydrogenase [NADP] cytoplasmic Unknown Unknown Unknown Cytoplasmic aconitate hydratase Pyruvic acid FADH2 Pyruvic acid CoA NAD Acetyl-CoA CO2 NADH H2O Oxalacetic acid Citric acid CoA Isocitric acid NAD Oxoglutaric acid CO2 NADH H+ NAD CoA Succinyl-CoA NADH H+ CO2 Pi GDP Succinic acid CoA GTP L-Malic acid Fumaric acid H2O NAD NADH H+ ATP HCO3- ADP Pi Q FAD QH2 cis-Aconitic acid H2O H2O NADPH Ammonium H+ L-Glutamic acid H2O NADP L-Glutamine H2O NH3 Isocitric acid NADP Oxoglutaric acid NADPH NADPH 2-Hydroxyglutarate NADP NADP Oxoglutaric acid NADPH NADP Oxoglutaric acid NADPH Citric acid Citric acid Thiamine pyrophosphate Lipoamide FAD Magnesium Thiamine pyrophosphate Lipoamide FAD Biotin Manganese 4Fe-4S 4Fe-4S Magnesium 4Fe-4S Glycolysis Mitochondrial Electron Transport Chain Inner mitochondrial membrane Mitochondrial intermembrane space Cytosol Mitochondrial matrix Mitochondrion Intracellular Space Inner mitochondrial membrane Outer mitochondrial membrane Cytosol Epigenetic Regulation Oncogene Activation, Tumour-suppressor inactivation TCA cycle Citric acid Isocitric acid Oxoglutaric acid 2-Hydroxyglutarate Cytoplasmic aconitate hydratase Isocitrate dehydrogenase [NADP] cytoplasmic mutIDH1 Methylcystosine dioxygenase TET1 Lysine-specific demethylase 2A
Mitochondria Mdh2 Unknown Unknown Mpc1 Pdha1 Cs Idh3a Idh3B Idh3g Ogdh Suclg1 Suclg2 Fh Pc Sdha Sdhb Sdhc Sdhd Aco2 Aco2 Unknown Gls2 Idh1 Unknown Unknown Unknown Aco1 Pyruvic acid FADH Pyruvic acid Coenzyme A NAD Acetyl-CoA Carbon dioxide NADH Water Oxalacetic acid Citric acid Coenzyme A Isocitric acid NAD Oxoglutaric acid Carbon dioxide NADH Hydrogen Ion NAD Coenzyme A Succinyl-CoA NADH Hydrogen Ion Carbon dioxide Phosphate Guanosine diphosphate Succinic acid Coenzyme A Guanosine triphosphate L-Malic acid Fumaric acid Water NAD NADH Hydrogen Ion Adenosine triphosphate Hydrogen carbonate Adenosine diphosphate Phosphate Coenzyme Q10 FAD QH(2) cis-Aconitic acid Water Water NADPH Ammonium Hydrogen Ion L-Glutamic acid Water NADP L-Glutamine Water Ammonia Isocitric acid NADP Oxoglutaric acid NADPH NADPH 2- Hydroxyglutarate NADP NADP Oxoglutaric acid NADPH NADP Oxoglutaric acid NADPH Citric acid Citric acid Glycolysis Mitochondrial Electron Transport Chain
Mdh2 Mpc1 Pdha1 Cs Idh3a Idh3B Idh3g Ogdh Suclg1 Suclg2 Fh Pc Sdha Sdhb Sdhc Sdhd Aco2 Aco2 Gls2 Idh1 Aco1 Pyr FADH2 Pyr CoA NAD Ac-CoA CO2 NADH H2O Oaa CA CoA I-cita NAD AKG CO2 NADH H+ NAD CoA Suc-CoA NADH H+ CO2 Pi GDP Succini CoA GTP Malate Fumarat H2O NAD NADH H+ ATP HCO3- ADP Pi Q FAD QH2 Aconiti H2O H2O NADPH Ammon H+ Glu H2O NADP Gln H2O NH3 I-cita NADP AKG NADPH NADPH 2HG NADP NADP AKG NADPH NADP AKG NADPH CA CA ThiamPP Lipoamd FAD Mg2+ ThiamPP Lipoamd FAD Biotin Mn2+ 4Fe-4S 4Fe-4S Mg2+ 4Fe-4S PW000146 PW000165 Inner mitochondrial membrane Mitochondrial intermembrane space Cytosol Mitochondrial matrix Mitochondrion Intracellular Space Inner mitochondrial membrane Outer mitochondrial membrane Cytosol Epigenetic Regulation Oncogene Activation, Tumour-suppressor inactivation TCA cycle Citric acid Isocitric acid Oxoglutaric acid 2-Hydroxyglutarate Cytoplasmic aconitate hydratase Isocitrate dehydrogenase [NADP] cytoplasmic mutIDH1 Methylcystosine dioxygenase TET1 Lysine-specific demethylase 2A
Mitochondria Mdh2 Mpc1 Pdha1 Cs Idh3a Idh3B Idh3g Ogdh Suclg1 Suclg2 Fh Pc Sdha Sdhb Sdhc Sdhd Aco2 Aco2 Gls2 Idh1 Aco1 Pyr FADH Pyr CoA NAD Ac-CoA CO2 NADH H2O Oaa CA CoA I-cita NAD AKG CO2 NADH H+ NAD CoA Suc-CoA NADH H+ CO2 Pi GDP Succini CoA GTP Malate Fumarat H2O NAD NADH H+ ATP HCO3 ADP Pi Coq FAD QH(2) Aconiti H2O H2O NADPH Ammon H+ Glu H2O NADP Gln H2O NH3 I-cita NADP AKG NADPH NADPH 2HG NADP NADP AKG NADPH NADP AKG NADPH CA CA PW000146 PW000165