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Cytosolic non-specific dipeptidase Carnosine synthase 1 Protein arginine N- methyltransferase 9 Cysteine sulfinic acid decarboxylase Histamine N- methyltransferase Amine oxidase [flavin- containing] A Succinate- semialdehyde dehydrogenase, mitochondrial Succinate- semialdehyde dehydrogenase, mitochondrial Histidine ammonia-lyase Urocanate hydratase Probable imidazolonepropionase Formimidoyltransferase- cyclodeaminase eIF-2-alpha kinase GCN2 eIF-2-alpha kinase GCN2 Amiloride- sensitive amine oxidase [copper- containing] Carnosine N- methyltransferase Carnosine synthase 1 Beta-Ala-His dipeptidase L-Glutamic acid Carnosine H2O β-Alanine Accumulation L-Histidine ATP β-Alanine ADP Pi S-Adenosylmethionine 3- Methylhistidine S-Adenosylhomocysteine Histamine CO2 S-Adenosylmethionine S-Adenosylhomocysteine 1-Methylhistamine H2O O2 Methylimidazole acetaldehyde NH3 H2O2 NADP H2O Methylimidazoleacetic acid NADPH H+ Imidazole-4-acetaldehyde NAD H2O Imidazoleacetic acid NADH H+ NH3 Urocanic acid 4-Imidazolone-5-propionic acid H2O H2O Formiminoglutamic acid Tetrahydrofolic acid 5-Formiminotetrahydrofolic acid ATP AMP PPi ATP AMP PPi H2O O2 NH3 H2O2 S- Adenosylmethionine S- Adenosylhomocysteine Anserine ATP 1-Methylhistidine β-Alanine ADP Pi H2O β-Alanine Zinc (II) ion Manganese Pyridoxal 5'-phosphate FAD NAD Zinc (II) ion Pyridoxal 5'-phosphate Copper Calcium Topaquinone tRNA(His) L- Histidyl- tRNA(His) tRNA(His) Glutamate Metabolism Manganese Manganese Intracellular Space Extracellular Space
Cndp2 Carns1 Prmt9 Csad Hnmt Maoa Aldh5a1 Aldh5a1 Hal Uroc1 Amdhd1 Ftcd Eif2ak4 Eif2ak4 Aoc1 Carnmt1 Carns1 Cndp1 L-Glutamic acid Carnosine Water β-Alanine Accumulation L-Histidine Adenosine triphosphate β-Alanine Adenosine diphosphate Phosphate S- Adenosylmethionine 3- Methylhistidine S- Adenosylhomocysteine Histamine Carbon dioxide S- Adenosylmethionine S- Adenosylhomocysteine 1- Methylhistamine Water Oxygen Methylimidazole acetaldehyde Ammonia Hydrogen peroxide NADP Water Methylimidazoleacetic acid NADPH Hydrogen Ion Imidazole-4- acetaldehyde NAD Water Imidazoleacetic acid NADH Hydrogen Ion Ammonia Urocanic acid 4- Imidazolone- 5-propionic acid Water Water Formiminoglutamic acid Tetrahydrofolic acid 5- Formiminotetrahydrofolic acid Adenosine triphosphate Adenosine monophosphate Pyrophosphate Adenosine triphosphate Adenosine monophosphate Pyrophosphate Water Oxygen Ammonia Hydrogen peroxide S- Adenosylmethionine S- Adenosylhomocysteine Anserine Adenosine triphosphate 1- Methylhistidine β-Alanine Adenosine diphosphate Phosphate Water β-Alanine tRNA(His) L- Histidyl- tRNA(His) tRNA(His) Glutamate Metabolism
Cndp2 Carns1 Prmt9 Csad Hnmt Maoa Aldh5a1 Aldh5a1 Hal Uroc1 Amdhd1 Ftcd Eif2ak4 Eif2ak4 Aoc1 Carnmt1 Carns1 Cndp1 Glu Carnosi H2O b-Ala Accumulation His ATP b-Ala ADP Pi SAMe 3-Mhis SAH Hsm CO2 SAMe SAH 1Mhis H2O O2 MetmAch NH3 H2O2 NADP H2O Mldzaa NADPH H+ Imd4aca NAD H2O Imaa NADH H+ NH3 Urocana 4Im-5pa H2O H2O FormGlu THFA 5-FTHA ATP AMP PPi ATP AMP PPi H2O O2 NH3 H2O2 SAMe SAH Anserin ATP 1-Mhis b-Ala ADP Pi H2O b-Ala Zinc Mn2+ Pyr-5'P FAD NAD Zinc Pyr-5'P Cu Ca2+ TopQne TRNAHIS LHTH TRNAHIS PW000003 Mn2+ Mn2+ Intracellular Space Extracellular Space
Cndp2 Carns1 Prmt9 Csad Hnmt Maoa Aldh5a1 Aldh5a1 Hal Uroc1 Amdhd1 Ftcd Eif2ak4 Eif2ak4 Aoc1 Carnmt1 Carns1 Cndp1 Glu Carnosi H2O b-Ala Accumulation His ATP b-Ala ADP Pi SAMe 3-Mhis SAH Hsm CO2 SAMe SAH 1Mhis H2O O2 MetmAch NH3 H2O2 NADP H2O Mldzaa NADPH H+ Imd4aca NAD H2O Imaa NADH H+ NH3 Urocana 4Im-5pa H2O H2O FormGlu THFA 5-FTHA ATP AMP Ppi ATP AMP Ppi H2O O2 NH3 H2O2 SAMe SAH Anserin ATP 1-Mhis b-Ala ADP Pi H2O b-Ala TRNAHIS LHTH TRNAHIS PW000003