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4-aminobutyrate
aminotransferase,
mitochondrial
Glutamate
decarboxylase 1
Asparagine
synthetase
[glutamine-
hydrolyzing]
Asparagine--
tRNA ligase,
cytoplasmic
Argininosuccinate
synthase
Aspartate--tRNA
ligase,
cytoplasmic
Amine oxidase
[flavin-
containing] B
Adenylosuccinate
lyase
D-aspartate
oxidase
Aspartoacylase
Adenylosuccinate
synthetase
isozyme 2
CAD protein
Isoaspartyl
peptidase/L-
asparaginase
Argininosuccinate
lyase
β-Alanine
L-Aspartic acid
Citrulline
Oxoglutaric acid
Malonic semialdehyde
L-Glutamic acid
CO
2
ATP
L-Glutamine
H
2
O
AMP
PP
i
L-Asparagine
L-Glutamic acid
ATP
AMP
PP
i
ATP
AMP
PP
i
Argininosuccinic acid
ATP
AMP
PP
i
H
2
O
O
2
Oxalacetic acid
NH
3
H
2
O
2
Fumaric acid
AMP
D-Aspartic acid
H
2
O
O
2
N-Acetyl-L-aspartic acid
H
2
O
Acetic acid
GTP
Inosinic acid
GDP
P
i
Dissipation
Adenylsuccinic acid
Carbamoyl
phosphate
P
i
Ureidosuccinic
acid
H
2
O
NH
3
L-Arginine
Pyridoxal
5'-phosphate
Pyridoxal
5'-phosphate
FAD
FAD
Zinc (II) ion
Magnesium
Zinc (II) ion
tRNA(Asn)
L-
Asparaginyl-
tRNA(Asn)
tRNA(Asp)
L- Aspartyl-
tRNA(Asp)
Pyrimidine
Metabolism
Pantothenate
and CoA
Biosynthesis
Histidine
Metabolism
Urea Cycle
Urea Cycle
Arginine and
Proline
Metabolism
beta-Alanine
Metabolism
Glycine and
Serine
Metabolism
Nicotinate and
Nicotinamide
Metabolism
Intracellular Space
Extracellular Space
Mitochondria
Lysosome
Peroxisome
Abat
Gad1
Asns
Nars
Ass1
Dars
Maob
Adsl
Ddo
Aspa
Adss
Cad
Asrgl1
Asl
β-Alanine
L-Aspartic acid
Citrulline
Oxoglutaric
acid
Malonic
semialdehyde
L-Glutamic acid
Carbon dioxide
Adenosine
triphosphate
L-Glutamine
Water
Adenosine
monophosphate
Pyrophosphate
L-Asparagine
L-Glutamic acid
Adenosine
triphosphate
Adenosine
monophosphate
Pyrophosphate
Adenosine
triphosphate
Adenosine
monophosphate
Pyrophosphate
Argininosuccinic
acid
Adenosine
triphosphate
Adenosine
monophosphate
Pyrophosphate
Water
Oxygen
Oxalacetic acid
Ammonia
Hydrogen
peroxide
Fumaric acid
Adenosine
monophosphate
D-Aspartic acid
Water
Oxygen
N-Acetyl-L-
aspartic acid
Water
Acetic acid
Guanosine
triphosphate
Inosinic acid
Guanosine
diphosphate
Phosphate
Dissipation
Adenylsuccinic
acid
Carbamoyl
phosphate
Phosphate
Ureidosuccinic
acid
Water
Ammonia
L-Arginine
tRNA(Asn)
L-
Asparaginyl-
tRNA(Asn)
tRNA(Asp)
L- Aspartyl-
tRNA(Asp)
Pyrimidine
Metabolism
Pantothenate
and CoA
Biosynthesis
Histidine
Metabolism
Urea Cycle
Urea Cycle
Arginine and
Proline
Metabolism
beta-Alanine
Metabolism
Glycine and
Serine
Metabolism
Nicotinate and
Nicotinamide
Metabolism