Toggle navigation
PathBank
Browse
Pathways
Table of Primary Pathways
Compounds
Proteins
Search
Advanced Text Search
ChemQuery Structure Search
Molecular Weight Search
Sequence Search
Analyze
Over-Representation Analysis
Path-MAP Analysis
Pathway Enrichment Analysis
About
About PathBank
Statistics
Style Guide
Other Databases
Pathway Legend
Pathway Category Definitions
PathWhiz
Downloads
Contact Us
Quantitative metabolomics services for biomarker discovery and validation.
Specializing in ready to use metabolomics kits.
Your source for quantitative metabolomics technologies and bioinformatics.
Loading Pathway...
Error: Pathway image not found.
Mitochondrial
uncoupling
protein 3
Argininosuccinate
synthase
Argininosuccinate
lyase
Carbamoyl-
phosphate
synthase
[ammonia],
mitochondrial
Glutamate
dehydrogenase
1,
mitochondrial
Ornithine
aminotransferase,
mitochondrial
Delta-1-
pyrroline-5-
carboxylate
dehydrogenase,
mitochondrial
Delta-1-
pyrroline-5-
carboxylate
dehydrogenase,
mitochondrial
Proline
dehydrogenase
1,
mitochondrial
Pyrroline-5-
carboxylate
reductase 2
Bifunctional
glutamate/proline-
-tRNA ligase
Prolyl
4-hydroxylase
subunit alpha-3
Proline
dehydrogenase
1,
mitochondrial
Pyrroline-5-
carboxylate
reductase 2
Probable
arginine--tRNA
ligase,
mitochondrial
Glycine
amidinotransferase,
mitochondrial
Guanidinoacetate
N-
methyltransferase
Creatine kinase
B-type
Arginase-1
Ornithine
carbamoyltransferase,
mitochondrial
D-amino-acid
oxidase
D-amino-acid
oxidase
Delta-1-
pyrroline-5-
carboxylate
dehydrogenase,
mitochondrial
Proline
dehydrogenase
1,
mitochondrial
Delta-1-
pyrroline-5-
carboxylate
dehydrogenase,
mitochondrial
Aspartate
aminotransferase,
cytoplasmic
Nitric oxide
synthase, brain
Fumaric acid
L-Aspartic acid
Ornithine
L-Arginine
Ornithine
Citrulline
Citrulline
ATP
AMP
PP
i
Argininosuccinic acid
ATP
NH
3
CO
2
H
2
O
ADP
Phosphoric acid
Carbamoyl
phosphate
L-Glutamic acid
H
2
O
NAD
Oxoglutaric
acid
NADH
Oxoglutaric
acid
L-Glutamic γ-semialdehyde
NAD
H
2
O
NADH
H
+
1-Pyrroline-5-carboxylic acid
NAD
H
2
O
NADH
L-Proline
NAD
NADH
ATP
AMP
PP
i
Oxoglutaric
acid
O
2
4-
Hydroxyproline
Succinic acid
CO
2
Pyrroline
hydroxycarboxylic
acid
NAD
NADH
ATP
AMP
PP
i
Glycine
Ornithine
Guanidoacetic
acid
S-Adenosylmethionine
S-Adenosylhomocysteine
Creatine
ATP
ADP
Phosphocreatine
H
2
O
Urea
P
i
D-Proline
H
2
O
O
2
1-Pyrroline-
2-carboxylic
acid
NH
3
H
2
O
2
H
2
O
O
2
1-Pyrroline-
4-hydroxy-2-
carboxylate
NH
3
H
2
O
2
NAD
H
2
O
4-Hydroxy-L-
glutamic acid
NADPH
L-4-
Hydroxyglutamate
semialdehyde
NAD
H
2
O
NADPH
Oxalacetic acid
4-Hydroxy-2-
oxoglutaric
acid
L-Aspartic acid
NADPH
O
2
N(omega)-Hydroxyarginine
Nitric oxide
NADP
H
2
O
Pyridoxal
5'-phosphate
FAD
FAD
Manganese
FAD
FAD
FAD
Pyridoxal
5'-phosphate
Heme
FAD
Flavin
Mononucleotide
Tetrahydrobiopterin
tRNA(Pro)
L-Prolyl-
tRNA(Pro)
tRNA(Arg)
L-Arginyl-
tRNA(Arg)
Citric Acid
Cycle
Alanine
Metabolism
D-Arginine and
D-Ornithine
Metabolism
D-Arginine and
D-Ornithine
Metabolism
Urea Cycle
Intracellular Space
Extracellular Space
Mitochondria
Lysosome
Mitochondria