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Alanine--tRNA
ligase,
cytoplasmic
Alanine
aminotransferase
1
Acetyl-CoA
carboxylase 2
Serine--
pyruvate
aminotransferase,
mitochondrial
Alanine--tRNA
ligase,
mitochondrial
Oxalacetic acid
L-Alanine
Pyruvic acid
Pyruvic acid
ATP
AMP
PP
i
Oxoglutaric
acid
L-Glutamic acid
ATP
HCO
3
-
ADP
P
i
L-Alanine
Accumulation
Glyoxylic acid
Glycine
ATP
AMP
PP
i
Zinc (II) ion
Pyridoxal
5'-phosphate
Biotin
Manganese
Pyridoxal
5'-phosphate
Zinc (II) ion
tRNA(Ala)
L-Alanyl-
tRNA(Ala)
tRNA(Ala)
L-Alanyl-
tRNA(Ala)
Citric Acid
Cycle
Selenoamino
Acid Metabolism
Mitochondria
Intracellular Space
Mitochondria
Aars
Gpt
Acacb
Agxt
Aars2
Oxalacetic acid
L-Alanine
Pyruvic acid
Pyruvic acid
Adenosine
triphosphate
Adenosine
monophosphate
Pyrophosphate
Oxoglutaric
acid
L-Glutamic acid
Adenosine
triphosphate
Hydrogen
carbonate
Adenosine
diphosphate
Phosphate
L-Alanine
Accumulation
Glyoxylic acid
Glycine
Adenosine
triphosphate
Adenosine
monophosphate
Pyrophosphate
tRNA(Ala)
L-Alanyl-
tRNA(Ala)
tRNA(Ala)
L-Alanyl-
tRNA(Ala)
Citric Acid
Cycle
Selenoamino
Acid Metabolism
Aars
Gpt
Acacb
Agxt
Aars2
Oaa
Ala
Pyr
Pyr
ATP
AMP
PP
i
AKG
Glu
ATP
HCO
3
-
ADP
P
i
Ala
Accumulation
Glyoxal
Gly
ATP
AMP
PP
i
Zinc
Pyr-5'P
Biotin
Mn2+
Pyr-5'P
Zinc
TRNAALA
LATA
TRNAALA
LATA
PW064439
PW064562
Mitochondria
Intracellular Space
Mitochondria
Aars
Gpt
Acacb
Agxt
Aars2
Oaa
Ala
Pyr
Pyr
ATP
AMP
Ppi
AKG
Glu
ATP
HCO3
ADP
Pi
Ala
Accumulation
Glyoxal
Gly
ATP
AMP
Ppi
TRNAALA
LATA
TRNAALA
LATA
PW064439
PW064562