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Search for 'valine AND leucine' in 'all pathways' in 'all' returned 488 results

SMP0000200 View Pathway	Metabolite Methylmalonic Aciduria Homo sapiens Matched Compounds: L-Leucine … L-Valine Matched Compound Synonyms: (2s)-alpha-leucine … (s)-(+)-leucine … (s)-leucine … Leucine … (2s)-a-leucine BioPAX SVG SBGN SBML PWML All files (.zip) Disease
SMP0000523 View Pathway	Metabolite Isobutyryl-CoA Dehydrogenase Deficiency Homo sapiens Matched Description: error of metabolism (IEM) of valine metabolism. It is an autosomal recessive disorder that is caused … the metabolism of branched-chain amino acids, specifically valine. This enzyme is responsible for … the third step in the breakdown of valine and converts isobutyryl-CoA into methylacrylyl-CoA. Defects … in the IBD enzyme function lead to elevated levels of valine in blood and other biofluids … energy. Treatment may include the use of L-carnitine supplements, frequent meals, and a low-valine diet. Matched Compounds: L-Leucine … L-Valine Matched Compound Synonyms: (2s)-alpha-leucine … (s)-(+)-leucine … (s)-leucine … Leucine … (2s)-a-leucine BioPAX SVG SBGN SBML PWML All files (.zip) Disease
SMP0120537 View Pathway	Metabolite Propionic Acidemia Mus musculus Matched Compounds: L-Valine … L-Leucine Matched Compound Synonyms: (s)-valine … Valine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine BioPAX SVG SBGN SBML PWML All files (.zip) Disease
SMP0120663 View Pathway	Metabolite 3-Methylglutaconic Aciduria Type I Rattus norvegicus Matched Compounds: L-Valine … L-Leucine Matched Compound Synonyms: (s)-valine … Valine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine BioPAX SVG SBGN SBML PWML All files (.zip) Disease
SMP0120665 View Pathway	Metabolite 3-Methylglutaconic Aciduria Type IV Rattus norvegicus Matched Compounds: L-Valine … L-Leucine Matched Compound Synonyms: (s)-valine … Valine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine BioPAX SVG SBGN SBML PWML All files (.zip) Disease
SMP0456532 View Pathway	Metabolite Secondary Metabolites: Valine and L-Leucine Biosynthesis from Pyruvate Morganella morganii subsp. morganii KT Matched Description: The biosynthesis of Valine and L-leucine from pyruvic acid starts with pyruvic acid interacting … -oxovaleric acid can produce an L-valine by interacting with a L-glutamic acid through a Valine … Transaminase resulting in the release of a Oxoglutaric acid and a L-valine. The 3-methyl-2-oxovaleric acid … with a L-glutamic acid through a branched-chain amino-acid aminotransferase resulting in the oxoglutaric acid and L-leucine. Matched Compounds: L-Valine … L-Leucine Matched Compound Synonyms: (s)-valine … Valine … L-valine … Keto-leucine … (2s)-alpha-leucine BioPAX SVG SBGN SBML PWML All files (.zip) Metabolic
SMP0452062 View Pathway	Metabolite Secondary Metabolites: Valine and L-Leucine Biosynthesis from Pyruvate Bradyrhizobium elkanii USDA 76 Matched Description: The biosynthesis of Valine and L-leucine from pyruvic acid starts with pyruvic acid interacting … -oxovaleric acid can produce an L-valine by interacting with a L-glutamic acid through a Valine … Transaminase resulting in the release of a Oxoglutaric acid and a L-valine. The 3-methyl-2-oxovaleric acid … with a L-glutamic acid through a branched-chain amino-acid aminotransferase resulting in the oxoglutaric acid and L-leucine. Matched Compounds: L-Valine … L-Leucine Matched Compound Synonyms: (s)-valine … Valine … L-valine … Keto-leucine … (2s)-alpha-leucine BioPAX SVG SBGN SBML PWML All files (.zip) Metabolic
SMP0454798 View Pathway	Metabolite Secondary Metabolites: Valine and L-Leucine Biosynthesis from Pyruvate Alloprevotella tannerae ATCC 51259 Matched Description: The biosynthesis of Valine and L-leucine from pyruvic acid starts with pyruvic acid interacting … -oxovaleric acid can produce an L-valine by interacting with a L-glutamic acid through a Valine … Transaminase resulting in the release of a Oxoglutaric acid and a L-valine. The 3-methyl-2-oxovaleric acid … with a L-glutamic acid through a branched-chain amino-acid aminotransferase resulting in the oxoglutaric acid and L-leucine. Matched Compounds: L-Valine … L-Leucine Matched Compound Synonyms: (s)-valine … Valine … L-valine … Keto-leucine … (2s)-alpha-leucine BioPAX SVG SBGN SBML PWML All files (.zip) Metabolic
SMP0457060 View Pathway	Metabolite Secondary Metabolites: Valine and L-Leucine Biosynthesis from Pyruvate Stenotrophomonas maltophilia D457 Matched Description: The biosynthesis of Valine and L-leucine from pyruvic acid starts with pyruvic acid interacting … -oxovaleric acid can produce an L-valine by interacting with a L-glutamic acid through a Valine … Transaminase resulting in the release of a Oxoglutaric acid and a L-valine. The 3-methyl-2-oxovaleric acid … with a L-glutamic acid through a branched-chain amino-acid aminotransferase resulting in the oxoglutaric acid and L-leucine. Matched Compounds: L-Valine … L-Leucine Matched Compound Synonyms: (s)-valine … Valine … L-valine … Keto-leucine … (2s)-alpha-leucine BioPAX SVG SBGN SBML PWML All files (.zip) Metabolic
SMP0464799 View Pathway	Metabolite Secondary Metabolites: Valine and L-Leucine Biosynthesis from Pyruvate Escherichia coli UMN026 Matched Description: The biosynthesis of Valine and L-leucine from pyruvic acid starts with pyruvic acid interacting … -oxovaleric acid can produce an L-valine by interacting with a L-glutamic acid through a Valine … Transaminase resulting in the release of a Oxoglutaric acid and a L-valine. The 3-methyl-2-oxovaleric acid … with a L-glutamic acid through a branched-chain amino-acid aminotransferase resulting in the oxoglutaric acid and L-leucine. Matched Compounds: L-Valine … L-Leucine Matched Compound Synonyms: (s)-valine … Valine … L-valine … Keto-leucine … (2s)-alpha-leucine BioPAX SVG SBGN SBML PWML All files (.zip) Metabolic