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Matched Description: first transported into the cell via the long-chain fatty acid transport protein 1 (FATP1). Once inside … . This reaction is facilitated by the long-chain fatty-acid CoA ligase 1 protein, which adds a CoA … acetyl-CoA carboxylase 1 to form malonyl-CoA, which inhibits the action of carnitine O … -palmitoyltransferase 1, thereby preventing 13-methyltetracosanoylcarnitine from forming and thereby preventing it from being transported into the mitochondria.

Matched Proteins: Long-chain-fatty-acid--CoA ligase 1 … Carnitine O-palmitoyltransferase 1, liver isoform … Acetyl-CoA carboxylase 1 … Long-chain fatty acid transport protein 1

Matched Protein Synonyms: Acyl-CoA synthetase 1 … LACS 1 … Long-chain acyl-CoA synthetase 1 … Palmitoyl-CoA ligase 1

Matched Compound Synonyms: 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine

Matched Description: transported into the cell via the long-chain fatty acid transport protein 1 (FATP1). Once inside … reaction is facilitated by the long-chain fatty-acid CoA ligase 1 protein, which adds a CoA moiety … carboxylase 1 to form malonyl-CoA, which inhibits the action of carnitine O-palmitoyltransferase 1

Matched Proteins: Long-chain-fatty-acid--CoA ligase 1 … Carnitine O-palmitoyltransferase 1, liver isoform … Acetyl-CoA carboxylase 1 … Long-chain fatty acid transport protein 1

Matched Protein Synonyms: Acyl-CoA synthetase 1 … LACS 1 … Long-chain acyl-CoA synthetase 1 … Palmitoyl-CoA ligase 1

Matched Compound Synonyms: 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine

Matched Description: first transported into the cell via the long-chain fatty acid transport protein 1 (FATP1). Once inside … . This reaction is facilitated by the long-chain fatty-acid CoA ligase 1 protein, which adds a CoA … acetyl-CoA carboxylase 1 to form malonyl-CoA, which inhibits the action of carnitine O … -palmitoyltransferase 1, thereby preventing 12-methyltetracosanoylcarnitine from forming and thereby preventing it from being transported into the mitochondria.

Matched Proteins: Long-chain-fatty-acid--CoA ligase 1 … Carnitine O-palmitoyltransferase 1, liver isoform … Acetyl-CoA carboxylase 1 … Long-chain fatty acid transport protein 1

Matched Protein Synonyms: Acyl-CoA synthetase 1 … LACS 1 … Long-chain acyl-CoA synthetase 1 … Palmitoyl-CoA ligase 1

Matched Compound Synonyms: 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine

Matched Description: first transported into the cell via the long-chain fatty acid transport protein 1 (FATP1). Once inside … . This reaction is facilitated by the long-chain fatty-acid CoA ligase 1 protein, which adds a CoA … acetyl-CoA carboxylase 1 to form malonyl-CoA, which inhibits the action of carnitine O … -palmitoyltransferase 1, thereby preventing 11-methylpentacosanoylcarnitine from forming and thereby preventing it from being transported into the mitochondria.

Matched Proteins: Long-chain-fatty-acid--CoA ligase 1 … Carnitine O-palmitoyltransferase 1, liver isoform … Acetyl-CoA carboxylase 1 … Long-chain fatty acid transport protein 1

Matched Protein Synonyms: Acyl-CoA synthetase 1 … LACS 1 … Long-chain acyl-CoA synthetase 1 … Palmitoyl-CoA ligase 1

Matched Compound Synonyms: 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine

Matched Description: first transported into the cell via the long-chain fatty acid transport protein 1 (FATP1). Once inside … . This reaction is facilitated by the long-chain fatty-acid CoA ligase 1 protein, which adds a CoA … acetyl-CoA carboxylase 1 to form malonyl-CoA, which inhibits the action of carnitine O … -palmitoyltransferase 1, thereby preventing 16-methylpentacosanoylcarnitine from forming and thereby preventing it from being transported into the mitochondria.

Matched Proteins: Long-chain-fatty-acid--CoA ligase 1 … Carnitine O-palmitoyltransferase 1, liver isoform … Acetyl-CoA carboxylase 1 … Long-chain fatty acid transport protein 1

Matched Protein Synonyms: Acyl-CoA synthetase 1 … LACS 1 … Long-chain acyl-CoA synthetase 1 … Palmitoyl-CoA ligase 1

Matched Compound Synonyms: 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium … 3-carboxy-2-hydroxy-n,n,n-trimethyl-1-propanaminium hydroxide, inner salt … 1-carnitine

Matched Proteins: Alanine aminotransferase 1 … Mitochondrial pyruvate carrier 1

Matched Protein Synonyms: GPT 1 … Glutamate pyruvate transaminase 1 … Glutamic--alanine transaminase 1 … Glutamic--pyruvic transaminase 1

Matched Compound Synonyms: 1-amino-propane-1,3-dicarboxylate … 1-amino-propane-1,3-dicarboxylic acid … 1-aminopropane-1,3-dicarboxylate … 1-aminopropane-1,3-dicarboxylic acid … Hydrocarbonate(1-)

Matched Description: involves undertaking a high-carbohydrate diet and, during severe attacks, a glucose 10% infusion. It is estimated that AIP affects 5.9 per 1 000 000 people.

Matched Proteins: Heme oxygenase 1

Matched Protein Synonyms: 5-aminolevulinic acid synthase 1 … Delta-ALA synthase 1 … Delta-aminolevulinate synthase 1 … HO-1

Matched Compound Synonyms: Succino-1-yl-coenzyme a … (sp-4-2)[7-ethenyl-17-formyl-12-[(4e,8e)-1-hydroxy-5,9,13-trimethyl-4,8,12-tetradecatrienyl]-3,8,13 … [sp-4-2-(e,e)]-[7-ethenyl-17-formyl-12-(1-hydroxy-5,9,13-trimethyl-4,8,12-tetradecatrienyl)-3,8,13 … 3-carbamoyl-1-beta-d-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt … 3-carbamoyl-1-beta-delta-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt

Matched Description: bone marrow transplants or stem cell treatment. It is estimated that CEP affects less than 1 in 1,000,000 individuals.

Matched Proteins: Heme oxygenase 1

Matched Protein Synonyms: 5-aminolevulinic acid synthase 1 … Delta-ALA synthase 1 … Delta-aminolevulinate synthase 1 … HO-1

Matched Compound Synonyms: Succino-1-yl-coenzyme a … (sp-4-2)[7-ethenyl-17-formyl-12-[(4e,8e)-1-hydroxy-5,9,13-trimethyl-4,8,12-tetradecatrienyl]-3,8,13 … [sp-4-2-(e,e)]-[7-ethenyl-17-formyl-12-(1-hydroxy-5,9,13-trimethyl-4,8,12-tetradecatrienyl)-3,8,13 … 3-carbamoyl-1-beta-d-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt … 3-carbamoyl-1-beta-delta-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt

Matched Description: antagonist of alpha-1 (α1), alpha-2 (α2), and histamine (H1) receptors. Blockade of these receptors

Matched Proteins: Voltage-dependent L-type calcium channel subunit beta-1 … Solute carrier family 22 member 1

Matched Protein Synonyms: Calcium channel, L type, alpha-1 polypeptide isoform 4 … Calcium channel voltage-dependent subunit beta 1 … Organic cation transporter 1 … Organic cation transporter 1

Matched Compound Synonyms: L-erythro-1-(2-amino-7,8-dihydro-4-hydroxy-6-pteridinyl)-1,2-propanediol

Matched Proteins: Inositol 1,4,5-trisphosphate receptor type 1 … Adenylate cyclase type 1 … Voltage-dependent L-type calcium channel subunit beta-1 … Guanine nucleotide-binding protein G(i) subunit alpha-1 … Guanine nucleotide-binding protein G(I)/G(S)/G(T) subunit beta-1

Matched Protein Synonyms: Tissue-specific extinguisher 1 … Tissue-specific extinguisher 1 … Calcium channel voltage-dependent subunit beta 1 … Tissue-specific extinguisher 1

Matched Compound Synonyms: Potassium ion(1+) … Potassium(1+) ion … Potassium(1+) … Potassium ion(1+) … Potassium(1+) ion