SMP0120503
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Isovaleric Aciduria
Mus musculus
Matched Compounds: 3-Methyl-1-hydroxybutyl-ThPP … 2-Methyl-1-hydroxypropyl-ThPP
Matched Proteins: Aldehyde oxidase 1 … Succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial
Matched Compound Synonyms: Thiamine(1+) diphosphoric acid … 3-carbamoyl-1-beta-d-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt … 3-carbamoyl-1-beta-delta-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt … 3-carbamoyl-1-d-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate … 3-carbamoyl-1-delta-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate
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SMP0120660
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2-Methyl-3-hydroxybutryl-CoA Dehydrogenase Deficiency
Rattus norvegicus
Matched Compounds: 3-Methyl-1-hydroxybutyl-ThPP … 2-Methyl-1-hydroxypropyl-ThPP
Matched Proteins: Aldehyde oxidase 1 … Succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial
Matched Compound Synonyms: Thiamine(1+) diphosphoric acid … 3-carbamoyl-1-beta-d-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt … 3-carbamoyl-1-beta-delta-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt … 3-carbamoyl-1-d-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate … 3-carbamoyl-1-delta-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate
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SMP0120679
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beta-Ketothiolase Deficiency
Rattus norvegicus
Matched Compounds: 3-Methyl-1-hydroxybutyl-ThPP … 2-Methyl-1-hydroxypropyl-ThPP
Matched Proteins: Aldehyde oxidase 1 … Succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial
Matched Compound Synonyms: Thiamine(1+) diphosphoric acid … 3-carbamoyl-1-beta-d-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt … 3-carbamoyl-1-beta-delta-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt … 3-carbamoyl-1-d-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate … 3-carbamoyl-1-delta-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate
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SMP0120443
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3-Methylglutaconic Aciduria Type III
Mus musculus
Matched Compounds: 3-Methyl-1-hydroxybutyl-ThPP … 2-Methyl-1-hydroxypropyl-ThPP
Matched Proteins: Aldehyde oxidase 1 … Succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial
Matched Compound Synonyms: Thiamine(1+) diphosphoric acid … 3-carbamoyl-1-beta-d-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt … 3-carbamoyl-1-beta-delta-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt … 3-carbamoyl-1-d-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate … 3-carbamoyl-1-delta-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate
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SMP0096785
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Cardiolipin Biosynthesis CL(14:0/18:1(9Z)/18:3(9Z,12Z,15Z)/18:3(9Z,12Z,15Z))
Drosophila melanogaster
Matched Description: enzyme glycerol-3-phosphate acyltransferase esterifies an acyl-group to the sn-1 position of sn … -glycerol 3-phosphate to form 1-acyl-sn-glycerol 3-phosphate (lysophosphatidic acid or LPA). Third, the … enzyme 1-acyl-sn-glycerol-3-phosphate acyltransferase converts LPA into phosphatidic acid (PA or 1,2
Matched Compounds: PA(14:0/18:1(9Z)) … CDP-DG(14:0/18:1(9Z)) … PGP(14:0/18:1(9Z)) … PG(14:0/18:1(9Z)) … CL(14:0/18:1(9Z)/18:3(9Z,12Z,15Z)/18:3(9Z,12Z,15Z))
Matched Compound Synonyms: 1-hydroxy-3-(phosphonooxy)-2-propanone … 1-hydroxy-3-(phosphonooxy)acetone … 1,3-dihydroxyacetone 1-phosphoric acid … 3-carbamoyl-1-beta-d-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt … 3-carbamoyl-1-beta-delta-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt
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SMP0096804
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Cardiolipin Biosynthesis CL(14:0/18:1(9Z)/20:4(5Z,8Z,11Z,14Z)/20:4(8Z,11Z,14Z,17Z))
Drosophila melanogaster
Matched Description: enzyme glycerol-3-phosphate acyltransferase esterifies an acyl-group to the sn-1 position of sn … -glycerol 3-phosphate to form 1-acyl-sn-glycerol 3-phosphate (lysophosphatidic acid or LPA). Third, the … enzyme 1-acyl-sn-glycerol-3-phosphate acyltransferase converts LPA into phosphatidic acid (PA or 1,2
Matched Compounds: PA(14:0/18:1(9Z)) … CDP-DG(14:0/18:1(9Z)) … PGP(14:0/18:1(9Z)) … PG(14:0/18:1(9Z)) … CL(14:0/18:1(9Z)/20:4(5Z,8Z,11Z,14Z)/20:4(8Z,11Z,14Z,17Z))
Matched Compound Synonyms: 1-hydroxy-3-(phosphonooxy)-2-propanone … 1-hydroxy-3-(phosphonooxy)acetone … 1,3-dihydroxyacetone 1-phosphoric acid … 3-carbamoyl-1-beta-d-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt … 3-carbamoyl-1-beta-delta-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt
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SMP0096950
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Cardiolipin Biosynthesis CL(14:0/20:1(11Z)/20:4(5Z,8Z,11Z,14Z)/22:0)
Drosophila melanogaster
Matched Description: enzyme glycerol-3-phosphate acyltransferase esterifies an acyl-group to the sn-1 position of sn … -glycerol 3-phosphate to form 1-acyl-sn-glycerol 3-phosphate (lysophosphatidic acid or LPA). Third, the … enzyme 1-acyl-sn-glycerol-3-phosphate acyltransferase converts LPA into phosphatidic acid (PA or 1,2
Matched Compounds: PA(14:0/20:1(11Z)) … CDP-DG(14:0/20:1(11Z)) … PGP(14:0/20:1(11Z)) … PG(14:0/20:1(11Z)) … CL(14:0/20:1(11Z)/20:4(5Z,8Z,11Z,14Z)/22:0)
Matched Compound Synonyms: 1-hydroxy-3-(phosphonooxy)-2-propanone … 1-hydroxy-3-(phosphonooxy)acetone … 1,3-dihydroxyacetone 1-phosphoric acid … 3-carbamoyl-1-beta-d-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt … 3-carbamoyl-1-beta-delta-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt
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SMP0096955
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Cardiolipin Biosynthesis CL(14:0/20:1(11Z)/22:0/22:0)
Drosophila melanogaster
Matched Description: enzyme glycerol-3-phosphate acyltransferase esterifies an acyl-group to the sn-1 position of sn … -glycerol 3-phosphate to form 1-acyl-sn-glycerol 3-phosphate (lysophosphatidic acid or LPA). Third, the … enzyme 1-acyl-sn-glycerol-3-phosphate acyltransferase converts LPA into phosphatidic acid (PA or 1,2
Matched Compounds: PA(14:0/20:1(11Z)) … CDP-DG(14:0/20:1(11Z)) … PGP(14:0/20:1(11Z)) … PG(14:0/20:1(11Z)) … CL(14:0/20:1(11Z)/22:0/22:0)
Matched Compound Synonyms: 1-hydroxy-3-(phosphonooxy)-2-propanone … 1-hydroxy-3-(phosphonooxy)acetone … 1,3-dihydroxyacetone 1-phosphoric acid … 3-carbamoyl-1-beta-d-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt … 3-carbamoyl-1-beta-delta-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt
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SMP0097112
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Cardiolipin Biosynthesis CL(14:1(9Z)/15:0/15:0/20:0)
Drosophila melanogaster
Matched Description: enzyme glycerol-3-phosphate acyltransferase esterifies an acyl-group to the sn-1 position of sn … -glycerol 3-phosphate to form 1-acyl-sn-glycerol 3-phosphate (lysophosphatidic acid or LPA). Third, the … enzyme 1-acyl-sn-glycerol-3-phosphate acyltransferase converts LPA into phosphatidic acid (PA or 1,2
Matched Compounds: LysoPA(14:1(9Z)/0:0) … PA(14:1(9Z)/15:0) … CDP-DG(14:1(9Z)/15:0) … PGP(14:1(9Z)/15:0) … PG(14:1(9Z)/15:0)
Matched Compound Synonyms: 1-hydroxy-3-(phosphonooxy)-2-propanone … 1-hydroxy-3-(phosphonooxy)acetone … 1,3-dihydroxyacetone 1-phosphoric acid … 3-carbamoyl-1-beta-d-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt … 3-carbamoyl-1-beta-delta-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt
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SMP0097220
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Cardiolipin Biosynthesis CL(14:1(9Z)/16:0/16:0/22:0)
Drosophila melanogaster
Matched Description: enzyme glycerol-3-phosphate acyltransferase esterifies an acyl-group to the sn-1 position of sn … -glycerol 3-phosphate to form 1-acyl-sn-glycerol 3-phosphate (lysophosphatidic acid or LPA). Third, the … enzyme 1-acyl-sn-glycerol-3-phosphate acyltransferase converts LPA into phosphatidic acid (PA or 1,2
Matched Compounds: LysoPA(14:1(9Z)/0:0) … PA(14:1(9Z)/16:0) … CDP-DG(14:1(9Z)/16:0) … PGP(14:1(9Z)/16:0) … PG(14:1(9Z)/16:0)
Matched Compound Synonyms: 1-hydroxy-3-(phosphonooxy)-2-propanone … 1-hydroxy-3-(phosphonooxy)acetone … 1,3-dihydroxyacetone 1-phosphoric acid … 3-carbamoyl-1-beta-d-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt … 3-carbamoyl-1-beta-delta-ribofuranosylpyridinium hydroxide 5'-ester with adenosine 5'-pyrophosphate inner salt
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