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Search for 'valine AND leucine' in 'all pathways' in 'all' returned 116 results

SMP0120459

Pw121710 View Pathway
Metabolite

beta-Ketothiolase Deficiency

Mus musculus

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine

  • Disease

    SMP0120444

    Pw121695 View Pathway
    Metabolite

    3-Methylglutaconic Aciduria Type IV

    Mus musculus

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine

  • Disease

    SMP0120805

    Pw122066 View Pathway
    Metabolite

    3-Hydroxyisobutyric Acid Dehydrogenase Deficiency

    Rattus norvegicus

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine

  • Disease

    SMP0120586

    Pw121842 View Pathway
    Metabolite

    3-Hydroxyisobutyric Acid Dehydrogenase Deficiency

    Mus musculus

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine

  • Disease

    SMP0120743

    Pw122004 View Pathway
    Metabolite

    Methylmalonate Semialdehyde Dehydrogenase Deficiency

    Rattus norvegicus

  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine

  • Disease

    SMP0087327

    Pw088346 View Pathway
    Metabolite

    Valine, Leucine, and Isoleucine Degradation

    Rattus norvegicus

  • Matched Description: Valine, isoleuciine, and leucine are essential amino acids and are identified as the branched-chain … protein breakdown. In muscle, the final products of leucine, isoleucine, and valine catabolism can be … dehydrogenase (BCKD), yielding the three different CoA derivatives. Isovaleryl-CoA is produced from leucine … by these two reactions, alpha-methylbutyryl-CoA from isoleucine, and isobutyryl-CoA from valine … breakdown pathways then diverge. Leucine is ultimately converted into acetyl-CoA and acetoacetate
  • Matched Compounds: L-Valine … L-Leucine
  • Matched Compound Synonyms: (s)-valineValine … L-valine … (2s)-alpha-leucine … (s)-(+)-leucine

  • Metabolic

    SMP0000524

    Pw000500 View Pathway
    Metabolite

    Isovaleric Acidemia

    Homo sapiens

  • Matched Description: (IEM) of leucine metabolism. It is an autosomal recessive disorder that is caused by a deficiency of … the conjugate. A diet that is also restricted in leucine consumption is also useful in treating the disorder.
  • Matched Compounds: L-Leucine … L-Valine
  • Matched Compound Synonyms: (2s)-alpha-leucine … (s)-(+)-leucine … (s)-leucineLeucine … (2s)-a-leucine

  • Disease

    SMP0000521

    Pw000497 View Pathway
    Metabolite

    3-Hydroxyisobutyric Acid Dehydrogenase Deficiency

    Homo sapiens

  • Matched Compounds: L-Leucine … L-Valine
  • Matched Compound Synonyms: (2s)-alpha-leucine … (s)-(+)-leucine … (s)-leucineLeucine … (2s)-a-leucine

  • Disease

    SMP0000236

    Pw000062 View Pathway
    Metabolite

    Propionic Acidemia

    Homo sapiens

  • Matched Compounds: L-Leucine … L-Valine
  • Matched Compound Synonyms: (2s)-alpha-leucine … (s)-(+)-leucine … (s)-leucineLeucine … (2s)-a-leucine

  • Disease

    SMP0000141

    Pw000214 View Pathway
    Metabolite

    3-Methylglutaconic Aciduria Type IV

    Homo sapiens

  • Matched Compounds: L-Leucine … L-Valine
  • Matched Compound Synonyms: (2s)-alpha-leucine … (s)-(+)-leucine … (s)-leucineLeucine … (2s)-a-leucine

  • Disease